Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru

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Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with mo...

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Detalles Bibliográficos
Autores: Cárdenas Ruiz de Castilla, Daniel, Chirinos Marroquín, Eliseo, Vergara Labrín, Marco, Del Castillo Parodi, Carlos
Formato: artículo
Fecha de Publicación:2018
Institución:Universidad de San Martín de Porres
Repositorio:Horizonte médico
Lenguaje:español
OAI Identifier:oai:horizontemedico.usmp.edu.pe:article/711
Enlace del recurso:https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711
Nivel de acceso:acceso abierto
Materia:Liver diseases
Polycystic liver
Laparoscopy
Hepatopatías
Hígado poliquistico
Laparoscopía
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spelling Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, PeruPoliquistosis hepática hemorrágica sin poliquistosis renal, una condición de alto riesgo vital: reporte de caso, abril 2015 PerúCárdenas Ruiz de Castilla, DanielChirinos Marroquín, EliseoVergara Labrín, MarcoDel Castillo Parodi, CarlosLiver diseasesPolycystic liverLaparoscopyHepatopatíasHígado poliquisticoLaparoscopíaPolycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with moderate sharp right upper quadrant abdominal pain and nausea for one hour. Emergency department: blood pressure 130/80 mmHg, heart rate 100 beats per minute, temperature 37 °C, O2 saturation 99 %, respiratory rate 22 breaths per minute. On examination, soft and relaxed abdomen, right upper quadrant abdominal pain, no visceromegaly, positive Murphy’s sign and rebound sign. Labs: hematocrit 34 %, hemoglobin 11.4 g/dL, white blood cells 12190, amylase 70 U/L. Abdominal ultrasound: Polycystic liver disease with ruptured cyst, abundant free subcapsular fluid within cavity, without pancreas and kidneys injury. Procedures: emergency exploratory laparoscopy, fluid drainage and aspiration, and partial cystectomy. Favorable evolution. Appointment with patient´s direct relatives for further studies.La poliquistosis hepática sin poliquistosis renal es una condición clínica infrecuente y más aún su complicación hemorrágica, con muy pocos casos reportados, siendo fatal sin tratamiento precoz. Mujer, 40 años, consulta por dolor en hipocondrio derecho, una hora de evolución, punzante, intensidad moderada; náuseas. En Emergencia: PA 130/80mmHg, FC 100 lpm, T 37°C, saturación O2 99 %, FR 22 rpm. Abdomen blando. Dolor en hipocondrio derecho. No visceromegalias. Punto cístico y signo de Murphy positivo. Laboratorio: Hematocrito 34 %, hemoglobina 11,4g/dL, leucocitos 12190, amilasa 70U/L. Ecografía Abdominal: Poliquistosis hepática con ruptura de quiste, líquido subcapsular y abundante libre en cavidad, sin lesiones en páncreas ni riñones. Se realiza laparoscopía exploradora de emergencia, drenaje y aspiración de líquido más quistectomía parcial. Evolución favorable, cita con familiares directos para estudios complementarios.Universidad de San Martín de Porres. Facultad de Medicina Humana2018-03-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdftext/htmlhttps://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/71110.24265/horizmed.2018.v18n1.12Horizonte Médico (Lima); Vol. 18 No. 1 (2018): January - March; 86-90Horizonte Médico (Lima); Vol. 18 Núm. 1 (2018): Enero - Marzo; 86-90Horizonte Médico (Lima); v. 18 n. 1 (2018): Enero - Marzo; 86-902227-35301727-558X10.24265/horizmed.2018.v18n1reponame:Horizonte médicoinstname:Universidad de San Martín de Porresinstacron:USMPspahttps://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/483https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/484Derechos de autor 2018 Horizonte Médico (Lima)https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessoai:horizontemedico.usmp.edu.pe:article/7112019-07-15T00:26:28Z
dc.title.none.fl_str_mv Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
Poliquistosis hepática hemorrágica sin poliquistosis renal, una condición de alto riesgo vital: reporte de caso, abril 2015 Perú
title Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
spellingShingle Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
Cárdenas Ruiz de Castilla, Daniel
Liver diseases
Polycystic liver
Laparoscopy
Hepatopatías
Hígado poliquistico
Laparoscopía
title_short Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
title_full Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
title_fullStr Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
title_full_unstemmed Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
title_sort Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
dc.creator.none.fl_str_mv Cárdenas Ruiz de Castilla, Daniel
Chirinos Marroquín, Eliseo
Vergara Labrín, Marco
Del Castillo Parodi, Carlos
author Cárdenas Ruiz de Castilla, Daniel
author_facet Cárdenas Ruiz de Castilla, Daniel
Chirinos Marroquín, Eliseo
Vergara Labrín, Marco
Del Castillo Parodi, Carlos
author_role author
author2 Chirinos Marroquín, Eliseo
Vergara Labrín, Marco
Del Castillo Parodi, Carlos
author2_role author
author
author
dc.subject.none.fl_str_mv Liver diseases
Polycystic liver
Laparoscopy
Hepatopatías
Hígado poliquistico
Laparoscopía
topic Liver diseases
Polycystic liver
Laparoscopy
Hepatopatías
Hígado poliquistico
Laparoscopía
description Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with moderate sharp right upper quadrant abdominal pain and nausea for one hour. Emergency department: blood pressure 130/80 mmHg, heart rate 100 beats per minute, temperature 37 °C, O2 saturation 99 %, respiratory rate 22 breaths per minute. On examination, soft and relaxed abdomen, right upper quadrant abdominal pain, no visceromegaly, positive Murphy’s sign and rebound sign. Labs: hematocrit 34 %, hemoglobin 11.4 g/dL, white blood cells 12190, amylase 70 U/L. Abdominal ultrasound: Polycystic liver disease with ruptured cyst, abundant free subcapsular fluid within cavity, without pancreas and kidneys injury. Procedures: emergency exploratory laparoscopy, fluid drainage and aspiration, and partial cystectomy. Favorable evolution. Appointment with patient´s direct relatives for further studies.
publishDate 2018
dc.date.none.fl_str_mv 2018-03-31
dc.type.none.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.none.fl_str_mv https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711
10.24265/horizmed.2018.v18n1.12
url https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711
identifier_str_mv 10.24265/horizmed.2018.v18n1.12
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/483
https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/484
dc.rights.none.fl_str_mv Derechos de autor 2018 Horizonte Médico (Lima)
https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Derechos de autor 2018 Horizonte Médico (Lima)
https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
text/html
dc.publisher.none.fl_str_mv Universidad de San Martín de Porres. Facultad de Medicina Humana
publisher.none.fl_str_mv Universidad de San Martín de Porres. Facultad de Medicina Humana
dc.source.none.fl_str_mv Horizonte Médico (Lima); Vol. 18 No. 1 (2018): January - March; 86-90
Horizonte Médico (Lima); Vol. 18 Núm. 1 (2018): Enero - Marzo; 86-90
Horizonte Médico (Lima); v. 18 n. 1 (2018): Enero - Marzo; 86-90
2227-3530
1727-558X
10.24265/horizmed.2018.v18n1
reponame:Horizonte médico
instname:Universidad de San Martín de Porres
instacron:USMP
instname_str Universidad de San Martín de Porres
instacron_str USMP
institution USMP
reponame_str Horizonte médico
collection Horizonte médico
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