Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru
Descripción del Articulo
Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with mo...
Autores: | , , , |
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Formato: | artículo |
Fecha de Publicación: | 2018 |
Institución: | Universidad de San Martín de Porres |
Repositorio: | Horizonte médico |
Lenguaje: | español |
OAI Identifier: | oai:horizontemedico.usmp.edu.pe:article/711 |
Enlace del recurso: | https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711 |
Nivel de acceso: | acceso abierto |
Materia: | Liver diseases Polycystic liver Laparoscopy Hepatopatías Hígado poliquistico Laparoscopía |
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Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, PeruPoliquistosis hepática hemorrágica sin poliquistosis renal, una condición de alto riesgo vital: reporte de caso, abril 2015 PerúCárdenas Ruiz de Castilla, DanielChirinos Marroquín, EliseoVergara Labrín, MarcoDel Castillo Parodi, CarlosLiver diseasesPolycystic liverLaparoscopyHepatopatíasHígado poliquisticoLaparoscopíaPolycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with moderate sharp right upper quadrant abdominal pain and nausea for one hour. Emergency department: blood pressure 130/80 mmHg, heart rate 100 beats per minute, temperature 37 °C, O2 saturation 99 %, respiratory rate 22 breaths per minute. On examination, soft and relaxed abdomen, right upper quadrant abdominal pain, no visceromegaly, positive Murphy’s sign and rebound sign. Labs: hematocrit 34 %, hemoglobin 11.4 g/dL, white blood cells 12190, amylase 70 U/L. Abdominal ultrasound: Polycystic liver disease with ruptured cyst, abundant free subcapsular fluid within cavity, without pancreas and kidneys injury. Procedures: emergency exploratory laparoscopy, fluid drainage and aspiration, and partial cystectomy. Favorable evolution. Appointment with patient´s direct relatives for further studies.La poliquistosis hepática sin poliquistosis renal es una condición clínica infrecuente y más aún su complicación hemorrágica, con muy pocos casos reportados, siendo fatal sin tratamiento precoz. Mujer, 40 años, consulta por dolor en hipocondrio derecho, una hora de evolución, punzante, intensidad moderada; náuseas. En Emergencia: PA 130/80mmHg, FC 100 lpm, T 37°C, saturación O2 99 %, FR 22 rpm. Abdomen blando. Dolor en hipocondrio derecho. No visceromegalias. Punto cístico y signo de Murphy positivo. Laboratorio: Hematocrito 34 %, hemoglobina 11,4g/dL, leucocitos 12190, amilasa 70U/L. Ecografía Abdominal: Poliquistosis hepática con ruptura de quiste, líquido subcapsular y abundante libre en cavidad, sin lesiones en páncreas ni riñones. Se realiza laparoscopía exploradora de emergencia, drenaje y aspiración de líquido más quistectomía parcial. Evolución favorable, cita con familiares directos para estudios complementarios.Universidad de San Martín de Porres. Facultad de Medicina Humana2018-03-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdftext/htmlhttps://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/71110.24265/horizmed.2018.v18n1.12Horizonte Médico (Lima); Vol. 18 No. 1 (2018): January - March; 86-90Horizonte Médico (Lima); Vol. 18 Núm. 1 (2018): Enero - Marzo; 86-90Horizonte Médico (Lima); v. 18 n. 1 (2018): Enero - Marzo; 86-902227-35301727-558X10.24265/horizmed.2018.v18n1reponame:Horizonte médicoinstname:Universidad de San Martín de Porresinstacron:USMPspahttps://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/483https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/484Derechos de autor 2018 Horizonte Médico (Lima)https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessoai:horizontemedico.usmp.edu.pe:article/7112019-07-15T00:26:28Z |
dc.title.none.fl_str_mv |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru Poliquistosis hepática hemorrágica sin poliquistosis renal, una condición de alto riesgo vital: reporte de caso, abril 2015 Perú |
title |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
spellingShingle |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru Cárdenas Ruiz de Castilla, Daniel Liver diseases Polycystic liver Laparoscopy Hepatopatías Hígado poliquistico Laparoscopía |
title_short |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
title_full |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
title_fullStr |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
title_full_unstemmed |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
title_sort |
Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru |
dc.creator.none.fl_str_mv |
Cárdenas Ruiz de Castilla, Daniel Chirinos Marroquín, Eliseo Vergara Labrín, Marco Del Castillo Parodi, Carlos |
author |
Cárdenas Ruiz de Castilla, Daniel |
author_facet |
Cárdenas Ruiz de Castilla, Daniel Chirinos Marroquín, Eliseo Vergara Labrín, Marco Del Castillo Parodi, Carlos |
author_role |
author |
author2 |
Chirinos Marroquín, Eliseo Vergara Labrín, Marco Del Castillo Parodi, Carlos |
author2_role |
author author author |
dc.subject.none.fl_str_mv |
Liver diseases Polycystic liver Laparoscopy Hepatopatías Hígado poliquistico Laparoscopía |
topic |
Liver diseases Polycystic liver Laparoscopy Hepatopatías Hígado poliquistico Laparoscopía |
description |
Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with moderate sharp right upper quadrant abdominal pain and nausea for one hour. Emergency department: blood pressure 130/80 mmHg, heart rate 100 beats per minute, temperature 37 °C, O2 saturation 99 %, respiratory rate 22 breaths per minute. On examination, soft and relaxed abdomen, right upper quadrant abdominal pain, no visceromegaly, positive Murphy’s sign and rebound sign. Labs: hematocrit 34 %, hemoglobin 11.4 g/dL, white blood cells 12190, amylase 70 U/L. Abdominal ultrasound: Polycystic liver disease with ruptured cyst, abundant free subcapsular fluid within cavity, without pancreas and kidneys injury. Procedures: emergency exploratory laparoscopy, fluid drainage and aspiration, and partial cystectomy. Favorable evolution. Appointment with patient´s direct relatives for further studies. |
publishDate |
2018 |
dc.date.none.fl_str_mv |
2018-03-31 |
dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.none.fl_str_mv |
https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711 10.24265/horizmed.2018.v18n1.12 |
url |
https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711 |
identifier_str_mv |
10.24265/horizmed.2018.v18n1.12 |
dc.language.none.fl_str_mv |
spa |
language |
spa |
dc.relation.none.fl_str_mv |
https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/483 https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711/484 |
dc.rights.none.fl_str_mv |
Derechos de autor 2018 Horizonte Médico (Lima) https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Derechos de autor 2018 Horizonte Médico (Lima) https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf text/html |
dc.publisher.none.fl_str_mv |
Universidad de San Martín de Porres. Facultad de Medicina Humana |
publisher.none.fl_str_mv |
Universidad de San Martín de Porres. Facultad de Medicina Humana |
dc.source.none.fl_str_mv |
Horizonte Médico (Lima); Vol. 18 No. 1 (2018): January - March; 86-90 Horizonte Médico (Lima); Vol. 18 Núm. 1 (2018): Enero - Marzo; 86-90 Horizonte Médico (Lima); v. 18 n. 1 (2018): Enero - Marzo; 86-90 2227-3530 1727-558X 10.24265/horizmed.2018.v18n1 reponame:Horizonte médico instname:Universidad de San Martín de Porres instacron:USMP |
instname_str |
Universidad de San Martín de Porres |
instacron_str |
USMP |
institution |
USMP |
reponame_str |
Horizonte médico |
collection |
Horizonte médico |
repository.name.fl_str_mv |
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repository.mail.fl_str_mv |
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13.754616 |
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La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).