Hemorrhagic polycystic liver disease without the presence of polycystic kidney disease, a serious life-threatening condition: A case report. April 2015, Peru

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Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with mo...

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Detalles Bibliográficos
Autores: Cárdenas Ruiz de Castilla, Daniel, Chirinos Marroquín, Eliseo, Vergara Labrín, Marco, Del Castillo Parodi, Carlos
Formato: artículo
Fecha de Publicación:2018
Institución:Universidad de San Martín de Porres
Repositorio:Horizonte médico
Lenguaje:español
OAI Identifier:oai:horizontemedico.usmp.edu.pe:article/711
Enlace del recurso:https://www.horizontemedico.usmp.edu.pe/index.php/horizontemed/article/view/711
Nivel de acceso:acceso abierto
Materia:Liver diseases
Polycystic liver
Laparoscopy
Hepatopatías
Hígado poliquistico
Laparoscopía
Descripción
Sumario:Polycystic liver disease without the presence of polycystic kidney disease is a rare clinical condition and its hemorrhagic complication is even rarer, with very few cases being reported. It can be life-threatening without a rapid intervention. Case report: A 40 year-old female who presented with moderate sharp right upper quadrant abdominal pain and nausea for one hour. Emergency department: blood pressure 130/80 mmHg, heart rate 100 beats per minute, temperature 37 °C, O2 saturation 99 %, respiratory rate 22 breaths per minute. On examination, soft and relaxed abdomen, right upper quadrant abdominal pain, no visceromegaly, positive Murphy’s sign and rebound sign. Labs: hematocrit 34 %, hemoglobin 11.4 g/dL, white blood cells 12190, amylase 70 U/L. Abdominal ultrasound: Polycystic liver disease with ruptured cyst, abundant free subcapsular fluid within cavity, without pancreas and kidneys injury. Procedures: emergency exploratory laparoscopy, fluid drainage and aspiration, and partial cystectomy. Favorable evolution. Appointment with patient´s direct relatives for further studies.
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