Presentación atípica del síndrome de Gorham-Stout. Caso clínico

• Autores: González Luna, Alejandro, Nuñez Pizarro, Jorge Luis, Rodríguez Echegaray, Clodo Iván
• Formato: artículo
• Fecha de Publicación: 2015
• Institución: Universidad Peruana de Ciencias Aplicadas
• Repositorio: UPC-Institucional
• Lenguaje: español
• OAI Identifier: oai:repositorioacademico.upc.edu.pe:10757/555429
• Enlace del recurso: http://hdl.handle.net/10757/555429
• Nivel de acceso: acceso abierto
• Materia: Enfermedad de Gorham-Stout; Osteólisis esencial;; Linfangioma; Lymphangioma; Gorham-Stout disease; Essential osteolysis

Gorham-Stout syndrome is an extremely rare pathology, of unknown etiology. It is characterized by proliferation of vascular channels that causes destruction and reabsorption of the bone matrix. We present a nine year-old male patient with an acute episode characterized by fever, chest pain, respiratory distress and dyspnea. The patient was submitted to computed tomography scan and a biopsy. The findings in the biopsy were multiple lytic lesions, osteolysis, and a mediastinal lymphangioma (lymphangiomatosis). The diagnosis was Gorham-Stout syndrome with atypical presentation.