Mid-ventricular hypertrophic cardiomyopathy with apical aneurysm: a multimodality imaging case report

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Mid-ventricular hypertrophic cardiomyopathy is a rare subgroup within hypertrophic cardiomyopathies that may present with apical aneurysm. This condition is associated with an increased risk of cardiac adverse events, including cardiac arrest, heart failure, thromboembolic events, or sudden cardiac...

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Detalles Bibliográficos
Autores: Martinez-Dominguez, Pavel, Horna-Noriega, Manuel, Santa-Ana-bayona, María José, Ramírez-Flores, Sara, Horna-Regalado, Lucia, Espinola-Zavaleta, Nilda
Formato: artículo
Fecha de Publicación:2025
Institución:Universidad Peruana de Ciencias Aplicadas
Repositorio:UPC-Institucional
Lenguaje:inglés
OAI Identifier:oai:repositorioacademico.upc.edu.pe:10757/684684
Enlace del recurso:http://hdl.handle.net/10757/684684
Nivel de acceso:acceso abierto
Materia:Defibrillators
Echocardiography
Hypertrophy
Implantable
Left Ventricular
Descripción
Sumario:Mid-ventricular hypertrophic cardiomyopathy is a rare subgroup within hypertrophic cardiomyopathies that may present with apical aneurysm. This condition is associated with an increased risk of cardiac adverse events, including cardiac arrest, heart failure, thromboembolic events, or sudden cardiac death. We present a case of a 41-year-old man who presented with a history of exertional dyspnea and syncope. Multimodality imaging with echocardiography and cardiac magnetic resonance showed hypertrophy of the mid-ventricular segments with apical aneurysm. An implantable cardioverter-defibrillator was implanted to prevent sudden cardiac death.
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