Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.

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Low-grade fibromyxoid sarcoma (LGFMS) is a soft tissue tumor of mesenchymal origin. Sarcomas are a heterogeneous group, representing 1% of all neoplasm diagnoses. Primary sarcomas of the central nervous system (CNS) are rare, and represent only 0.7% of all sarcomas, with an estimated incidence of 3...

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Detalles Bibliográficos
Autores: León-Palacios, José L., Palacios M, Augusto M., Casavilca-Zambrano, Sandro, Darío Esteban-Arias, Darío, Sánchez A, Sandro E., Alaba G, Wesley, Pineda G, Ronald A.
Formato: artículo
Fecha de Publicación:2020
Institución:Universidad Peruana Cayetano Heredia
Repositorio:Revistas - Universidad Peruana Cayetano Heredia
Lenguaje:español
OAI Identifier:oai:revistas.upch.edu.pe:article/3800
Enlace del recurso:https://revistas.upch.edu.pe/index.php/RNP/article/view/3800
Nivel de acceso:acceso abierto
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spelling Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.Sarcoma fibromixoide intracraneal primario de bajo grado: reporte de caso y revisión de la literatura.León-Palacios, José L.Palacios M, Augusto M.Casavilca-Zambrano, SandroDarío Esteban-Arias, DaríoSánchez A, Sandro E.Alaba G, WesleyPineda G, Ronald A.Low-grade fibromyxoid sarcoma (LGFMS) is a soft tissue tumor of mesenchymal origin. Sarcomas are a heterogeneous group, representing 1% of all neoplasm diagnoses. Primary sarcomas of the central nervous system (CNS) are rare, and represent only 0.7% of all sarcomas, with an estimated incidence of 3 per 10 million people per year. The case of a 59-year-old woman who developed a low-grade intracranial fibromyxoid sarcoma in the right parietal region, is described. The clinical course, imaging studies, histopathological features, and treatment approach of this unusual diagnosis, are discussed. Low-grade intracranial fibromyxoid sarcoma is a rare and probably under- reported condition. The definitive diagnosis is usually made through histo-pathological studies.El sarcoma fibromixoide de bajo grado (LGFMS) es un tumor de tejidos blandos de origen mesenquimal. Los sarcomas son un grupo heterogéneo, que representa el 1% de todas las neoplasias. Los sarcomas primarios del sistema nervioso central (SNC) son raros y representan solo el 0,7% del total de sarcomas, con una incidencia estimada de 3 por cada 10 millones de personas por año. En este artículo, se describe el caso de una mujer de 59 años que presentó un sarcoma fibromixoide intracraneal de bajo grado, localizado en la región parietal derecha. Se discute el curso clínico, estudios de imágenes, características histopatológicas y tratamiento de este diagnóstico infrecuente y, por lo mismo, muy poco reportado. El diagnóstico definitivo se obtiene, ciertamente, mediante estudios histo- patológicos.Universidad Peruana Cayetano Heredia2020-10-09info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://revistas.upch.edu.pe/index.php/RNP/article/view/380010.20453/rnp.v83i3.3800Revista de Neuro-Psiquiatria; Vol. 83 No. 3 (2020): July - September (pre-print); 203-207Revista de Neuro-Psiquiatría; Vol. 83 Núm. 3 (2020): Julio-Setiembre; 203-207Revista de Neuro-Psiquiatria; v. 83 n. 3 (2020): Julio-Setiembre; 203-2071609-73940034-8597reponame:Revistas - Universidad Peruana Cayetano Herediainstname:Universidad Peruana Cayetano Herediainstacron:UPCHspahttps://revistas.upch.edu.pe/index.php/RNP/article/view/3800/4280info:eu-repo/semantics/openAccessoai:revistas.upch.edu.pe:article/38002020-10-10T04:43:49Z
dc.title.none.fl_str_mv Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
Sarcoma fibromixoide intracraneal primario de bajo grado: reporte de caso y revisión de la literatura.
title Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
spellingShingle Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
León-Palacios, José L.
title_short Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
title_full Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
title_fullStr Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
title_full_unstemmed Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
title_sort Low-grade fibro-myxoid sarcoma of intracranial origin: A case report and literature review.
dc.creator.none.fl_str_mv León-Palacios, José L.
Palacios M, Augusto M.
Casavilca-Zambrano, Sandro
Darío Esteban-Arias, Darío
Sánchez A, Sandro E.
Alaba G, Wesley
Pineda G, Ronald A.
author León-Palacios, José L.
author_facet León-Palacios, José L.
Palacios M, Augusto M.
Casavilca-Zambrano, Sandro
Darío Esteban-Arias, Darío
Sánchez A, Sandro E.
Alaba G, Wesley
Pineda G, Ronald A.
author_role author
author2 Palacios M, Augusto M.
Casavilca-Zambrano, Sandro
Darío Esteban-Arias, Darío
Sánchez A, Sandro E.
Alaba G, Wesley
Pineda G, Ronald A.
author2_role author
author
author
author
author
author
description Low-grade fibromyxoid sarcoma (LGFMS) is a soft tissue tumor of mesenchymal origin. Sarcomas are a heterogeneous group, representing 1% of all neoplasm diagnoses. Primary sarcomas of the central nervous system (CNS) are rare, and represent only 0.7% of all sarcomas, with an estimated incidence of 3 per 10 million people per year. The case of a 59-year-old woman who developed a low-grade intracranial fibromyxoid sarcoma in the right parietal region, is described. The clinical course, imaging studies, histopathological features, and treatment approach of this unusual diagnosis, are discussed. Low-grade intracranial fibromyxoid sarcoma is a rare and probably under- reported condition. The definitive diagnosis is usually made through histo-pathological studies.
publishDate 2020
dc.date.none.fl_str_mv 2020-10-09
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://revistas.upch.edu.pe/index.php/RNP/article/view/3800
10.20453/rnp.v83i3.3800
url https://revistas.upch.edu.pe/index.php/RNP/article/view/3800
identifier_str_mv 10.20453/rnp.v83i3.3800
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv https://revistas.upch.edu.pe/index.php/RNP/article/view/3800/4280
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
dc.source.none.fl_str_mv Revista de Neuro-Psiquiatria; Vol. 83 No. 3 (2020): July - September (pre-print); 203-207
Revista de Neuro-Psiquiatría; Vol. 83 Núm. 3 (2020): Julio-Setiembre; 203-207
Revista de Neuro-Psiquiatria; v. 83 n. 3 (2020): Julio-Setiembre; 203-207
1609-7394
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collection Revistas - Universidad Peruana Cayetano Heredia
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