Adenosquamous carcinoma of the ampulla of Vater – an unusual neoplasia with poor prognosis

Descripción del Articulo

Adenosquamous carcinoma of the ampulla of Vater is a rare neoplasia (1% of incidence of all ampulla of Vater´s neoplasias), in which both glandular and squamous elements are histologically malignant. In this study, we report the case of a 61 years old woman who presented jaundice and abdominal pain....

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Detalles Bibliográficos
Autores: Revoredo Rego, Fernando, Tang Sing, Jorge, Uribe León, Mónica, Arenas Gamio, José, De Vinatea De Cárdenas, José
Formato: artículo
Fecha de Publicación:2014
Institución:Universidad Nacional Mayor de San Marcos
Repositorio:Revistas - Universidad Nacional Mayor de San Marcos
Lenguaje:español
OAI Identifier:oai:ojs.csi.unmsm:article/9783
Enlace del recurso:https://revistasinvestigacion.unmsm.edu.pe/index.php/anales/article/view/9783
Nivel de acceso:acceso abierto
Materia:Adenosquamous carcinoma of the ampulla of Vater
pancreaticoduodenectomy.
Carcinoma adenoescamoso de la ampolla de Vater
pancreaticoduodenectomía.
Descripción
Sumario:Adenosquamous carcinoma of the ampulla of Vater is a rare neoplasia (1% of incidence of all ampulla of Vater´s neoplasias), in which both glandular and squamous elements are histologically malignant. In this study, we report the case of a 61 years old woman who presented jaundice and abdominal pain. The patient was diagnosed with adenocarcinoma of the ampulla of Vater and underwent pancreaticoduodenectomy. A R0 (no residual disease by microscopy) resection was performed. The final diagnosis was adenosquamous carcinoma of the ampulla of Vater, T4N0Mx. Two and one half months later she had multiple liver metastases and died 3 months after surgery. An updated review of this unusual disease and of its dismal prognosis is made.
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