Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
Descripción del Articulo
We report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorect...
Autores: | , , , , |
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Formato: | artículo |
Fecha de Publicación: | 2023 |
Institución: | Colegio Médico del Perú |
Repositorio: | Acta Médica Peruana |
Lenguaje: | inglés español |
OAI Identifier: | oai:amp.cmp.org.pe:article/2580 |
Enlace del recurso: | https://amp.cmp.org.pe/index.php/AMP/article/view/2580 |
Nivel de acceso: | acceso abierto |
Materia: | Trombastenia de Glanzmann Factor VII recombinante Histerectomía Perú Glanzmann's thrombasthenia Recombinant factor VII Hysterectomy Peru |
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Successful outcomes of surgery procedures in patient with Glanzmann´s ThrombastheniaResultados exitosos de procedimientos quirúrgicos en paciente con trombastenia de GlanzmannGuerrero Arismendiz, Bruno RenatoJavier-Najarro, RosarioDíaz-Torres, CarlosPeñaloza-Maquera, SaulCornejo-Salazar, Jose LuisGuerrero Arismendiz, Bruno RenatoJavier-Najarro, RosarioDíaz-Torres, CarlosPeñaloza-Maquera, SaulCornejo-Salazar, Jose LuisTrombastenia de GlanzmannFactor VII recombinanteHisterectomíaPerúGlanzmann's thrombastheniaRecombinant factor VIIHysterectomyPeruWe report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorectomy was proposed and recombinant factor VII was required. Surgical and postoperative outcomes were successful, without surgical complications, bleeding, or hemogram alterations. 4 years later, she required tooth extraction because of periodontal disease and pulp necrosis. In Peru, reports of GT patients requiring major and minor surgical procedures are lacking, given the low disease prevalence and the difficulties related to surgery. The report of these successful cases becomes relevant to continue improving GT management.Presentamos el caso de una paciente de 35 años con trombastenia de Glanzmann (GT) y anemia severa por sangrado uterino anormal secundario a miomatosis uterina. Requirió varias admisiones de transfusiones de glóbulos rojos y plaquetas. Se propuso histerectomía subtotal electiva con salpingooforectomía y se requirió factor VII recombinante. Los resultados quirúrgicos y postoperatorios fueron exitosos, sin complicaciones quirúrgicas, sangrado ni alteraciones del hemograma. 4 años después, requirió extracción dental por enfermedad periodontal y necrosis pulpar. En Perú son escasos los reportes de pacientes con GT que requieren procedimientos quirúrgicos mayores y menores, dada la baja prevalencia de la enfermedad y las dificultades relacionadas con la cirugía. El reporte de estos casos de éxito cobra relevancia para seguir mejorando la gestión de GT.Colegio Médico del Perú2023-07-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdftext/htmltext/xmlhttps://amp.cmp.org.pe/index.php/AMP/article/view/258010.35663/amp.2023.402.2580ACTA MEDICA PERUANA; Vol. 40 No. 2 (2023): April - JuneACTA MEDICA PERUANA; Vol. 40 Núm. 2 (2023): Abril - Junio1728-59171018-8800reponame:Acta Médica Peruanainstname:Colegio Médico del Perúinstacron:CMPengspahttps://amp.cmp.org.pe/index.php/AMP/article/view/2580/1562https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1871https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1872Copyright (c) 2023 ACTA MEDICA PERUANAinfo:eu-repo/semantics/openAccessoai:amp.cmp.org.pe:article/25802024-11-29T17:51:29Z |
dc.title.none.fl_str_mv |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia Resultados exitosos de procedimientos quirúrgicos en paciente con trombastenia de Glanzmann |
title |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
spellingShingle |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia Guerrero Arismendiz, Bruno Renato Trombastenia de Glanzmann Factor VII recombinante Histerectomía Perú Glanzmann's thrombasthenia Recombinant factor VII Hysterectomy Peru |
title_short |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
title_full |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
title_fullStr |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
title_full_unstemmed |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
title_sort |
Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia |
dc.creator.none.fl_str_mv |
Guerrero Arismendiz, Bruno Renato Javier-Najarro, Rosario Díaz-Torres, Carlos Peñaloza-Maquera, Saul Cornejo-Salazar, Jose Luis Guerrero Arismendiz, Bruno Renato Javier-Najarro, Rosario Díaz-Torres, Carlos Peñaloza-Maquera, Saul Cornejo-Salazar, Jose Luis |
author |
Guerrero Arismendiz, Bruno Renato |
author_facet |
Guerrero Arismendiz, Bruno Renato Javier-Najarro, Rosario Díaz-Torres, Carlos Peñaloza-Maquera, Saul Cornejo-Salazar, Jose Luis |
author_role |
author |
author2 |
Javier-Najarro, Rosario Díaz-Torres, Carlos Peñaloza-Maquera, Saul Cornejo-Salazar, Jose Luis |
author2_role |
author author author author |
dc.subject.none.fl_str_mv |
Trombastenia de Glanzmann Factor VII recombinante Histerectomía Perú Glanzmann's thrombasthenia Recombinant factor VII Hysterectomy Peru |
topic |
Trombastenia de Glanzmann Factor VII recombinante Histerectomía Perú Glanzmann's thrombasthenia Recombinant factor VII Hysterectomy Peru |
description |
We report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorectomy was proposed and recombinant factor VII was required. Surgical and postoperative outcomes were successful, without surgical complications, bleeding, or hemogram alterations. 4 years later, she required tooth extraction because of periodontal disease and pulp necrosis. In Peru, reports of GT patients requiring major and minor surgical procedures are lacking, given the low disease prevalence and the difficulties related to surgery. The report of these successful cases becomes relevant to continue improving GT management. |
publishDate |
2023 |
dc.date.none.fl_str_mv |
2023-07-31 |
dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.none.fl_str_mv |
https://amp.cmp.org.pe/index.php/AMP/article/view/2580 10.35663/amp.2023.402.2580 |
url |
https://amp.cmp.org.pe/index.php/AMP/article/view/2580 |
identifier_str_mv |
10.35663/amp.2023.402.2580 |
dc.language.none.fl_str_mv |
eng spa |
language |
eng spa |
dc.relation.none.fl_str_mv |
https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1562 https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1871 https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1872 |
dc.rights.none.fl_str_mv |
Copyright (c) 2023 ACTA MEDICA PERUANA info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2023 ACTA MEDICA PERUANA |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf text/html text/xml |
dc.publisher.none.fl_str_mv |
Colegio Médico del Perú |
publisher.none.fl_str_mv |
Colegio Médico del Perú |
dc.source.none.fl_str_mv |
ACTA MEDICA PERUANA; Vol. 40 No. 2 (2023): April - June ACTA MEDICA PERUANA; Vol. 40 Núm. 2 (2023): Abril - Junio 1728-5917 1018-8800 reponame:Acta Médica Peruana instname:Colegio Médico del Perú instacron:CMP |
instname_str |
Colegio Médico del Perú |
instacron_str |
CMP |
institution |
CMP |
reponame_str |
Acta Médica Peruana |
collection |
Acta Médica Peruana |
repository.name.fl_str_mv |
|
repository.mail.fl_str_mv |
|
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1842710632043905024 |
score |
12.660197 |
Nota importante:
La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).
La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).