Maxillary osteogenic distraction and comprehensive orthodontic treatment in a patient with Pfeiffer syndrome. A case report

• Autores: Leiva, Noemí, Stange, Carolina, Ayala, Francisca, Fuentes, Vanessa, Gloria Morovic, Carmen
• Formato: artículo
• Fecha de Publicación: 2019
• Institución: Universidad Nacional Mayor de San Marcos
• Repositorio: Revista UNMSM - Odontología Sanmarquina
• Lenguaje: español
• OAI Identifier: oai:ojs.csi.unmsm:article/16712
• Enlace del recurso: https://revistasinvestigacion.unmsm.edu.pe/index.php/odont/article/view/16712
• Nivel de acceso: acceso abierto
• Materia: Acrocephalosyndactylia; Orthodontics; Distraction osteogenesis; Maxilla (source: MeSH NLM); Acrocefalosindactilia; Ortodoncia; Osteogénesis por distracción; Hueso maxilar (fuente: DeCS BIREME)

Pfeiffer´s syndrome is an autosomal dominantly inherited craniosynostosis, its clinical features are both at craniofacial level and upper and lower limbs. The treatment must be carried out by a multidisciplinary team and represents a great challenge for health professionals. The aim of this article is to present the case of a teenage patient diagnosed with Pfeiffer´s syndrome, who had severe maxillary hypoplasia, class III malocclusion and negative overjet; treated by osteogenic distraction with a RED (rigid external distractor) associated with fixed orthodontic appliances. The results reached the patient’s therapeutic and esthetic expectations and showed stability at 20 months posttreatment.