Fournier's gangrene in a child with Hyper Immunoglobulin E syndrome

• Autores: Pajares, Alejandro, Arias-Delgado, José Antonio, Imán-Izquierdo, Fernando Jeancarlos, Silva- Caso, Wilmer
• Formato: artículo
• Fecha de Publicación: 2023
• Institución: Universidad Peruana de Ciencias Aplicadas
• Repositorio: UPC-Institucional
• Lenguaje: inglés
• OAI Identifier: oai:repositorioacademico.upc.edu.pe:10757/668042
• Enlace del recurso: http://hdl.handle.net/10757/668042
• Nivel de acceso: acceso abierto
• Materia: Hyperimmunoglobulin E Syndrome; Job Syndrome; Immune Disorder; Connective Tissue Disorder; Invasive Infections; Fournier Gangrene; Necrotizing Fasciitis; Polymicrobial Etiology; Surgical Debridement; Scrotal Necrosis

Hyperimmunoglobulin E syndrome or Job syndrome is defined as an immune and connective tissue disorder that results in complications such as invasive infections. On the other hand, Fournier gangrene is a rapidly progressive necrotizing fasciitis that affects the perineal area, has a polymicrobial etiology, and its treatment consists of rapid and aggressive surgical debridement, antibiotic therapy, and hemodynamic support. We present the case of Fournier gangrene in an 11-year-old boy with a diagnosis of hyperimmunoglobulinemia E. who was admitted with scrotal necrosis with favorable evolution after initial medical management.