Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report

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Parasagittal meningiomas are intracranial tumors that develop along the superior sagittal sinus. Although they are generally benign, their proximity to vital vascular structures poses significant challenges for surgical management. In patients with neurofibromatosis type 2 (NF2), an autosomal domina...

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Detalles Bibliográficos
Autores: Aguilar, Luis, Váscones-Román , Fritz Fidel, Caucha Morales , Yelimer
Formato: artículo
Fecha de Publicación:2025
Institución:Universidad Peruana Cayetano Heredia
Repositorio:Revistas - Universidad Peruana Cayetano Heredia
Lenguaje:inglés
OAI Identifier:oai:revistas.upch.edu.pe:article/5841
Enlace del recurso:https://revistas.upch.edu.pe/index.php/RMH/article/view/5841
Nivel de acceso:acceso abierto
Materia:Neurofibromatosis 2
Meningioma
Brain neoplasms
meningioma
neuroma acústico
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spelling Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case ReportManejo neuroquirúrgico de un meningioma parasagital gigante en una paciente con neurofibromatosis tipo 2: reporte de casoAguilar, LuisVáscones-Román , Fritz FidelCaucha Morales , YelimerNeurofibromatosis 2MeningiomaBrain neoplasmsNeurofibromatosis 2meningiomaneuroma acústicoParasagittal meningiomas are intracranial tumors that develop along the superior sagittal sinus. Although they are generally benign, their proximity to vital vascular structures poses significant challenges for surgical management. In patients with neurofibromatosis type 2 (NF2), an autosomal dominant genetic disorder, there is a high predisposition to develop multiple tumors in the central nervous system, including meningiomas and schwannomas. The report discusses a 23-year-old woman with a family history of NF2 who presented with a large parasagittal meningioma and bilateral schwannomas, along with symptoms such as headaches, hearing loss, vertigo, and seizures. MRI revealed a right frontoparietal meningioma invading the superior sagittal sinus. Successful craniotomy and resection showed a poorly vascularized meningioma invading the sagittal sinus. This case highlights the surgical difficulties associated with sagittal sinus meningioma invasion and emphasizes the importance of multidisciplinary care and long-term follow-up due to the high risk of tumor recurrence in NF2 patients.Los meningiomas parasagitales son tumores intracraneales que se desarrollan a lo largo del seno sagital superior, y aunque generalmente son benignos, su proximidad a importantes estructuras vasculares presenta desafíos significativos para el manejo quirúrgico. En pacientes con neurofibromatosis tipo 2 (NF2), una enfermedad genética autosómica dominante, existe una alta predisposición a desarrollar múltiples tumores en el sistema nervioso central, incluidos meningiomas y schwannomas. Se presentó el caso de una mujer de 23 años con antecedentes familiares de NF2 quien presentó un meningioma parasagital gigante y schwannomas bilaterales, experimentando dolores de cabeza, pérdida de audición, vértigo y convulsiones. La resonancia magnética mostró la presencia de un meningioma frontoparietal derecho que invadía el seno sagital superior. La craneotomía y resección exitosa revelaron un meningioma poco vascularizado con invasión del seno sagital. Este caso subraya los desafíos quirúrgicos de la invasión del meningioma en el seno sagital, enfatizando la necesidad de atención multidisciplinaria y seguimiento a largo plazo debido al alto riesgo de recurrencia del tumor en pacientes con NF2.Universidad Peruana Cayetano Heredia2025-09-30info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed articleArtículo evaluado por paresapplication/pdfhttps://revistas.upch.edu.pe/index.php/RMH/article/view/584110.20453/rmh.v36i3.5841Revista Médica Herediana; Vol. 36 No. 3 (2025): Julio-septiembre; 247-251Revista Médica Herediana; Vol. 36 Núm. 3 (2025): Julio-septiembre; 247-251Revista Medica Herediana; v. 36 n. 3 (2025): Julio-septiembre; 247-2511729-214X1018-130X10.20453/rmh.v36i3reponame:Revistas - Universidad Peruana Cayetano Herediainstname:Universidad Peruana Cayetano Herediainstacron:UPCHenghttps://revistas.upch.edu.pe/index.php/RMH/article/view/5841/6692Derechos de autor 2025 Luis Aguilar, Fritz Vascones, Yelimer Caucha http://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessoai:revistas.upch.edu.pe:article/58412025-10-09T18:09:23Z
dc.title.none.fl_str_mv Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
Manejo neuroquirúrgico de un meningioma parasagital gigante en una paciente con neurofibromatosis tipo 2: reporte de caso
title Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
spellingShingle Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
Aguilar, Luis
Neurofibromatosis 2
Meningioma
Brain neoplasms
Neurofibromatosis 2
meningioma
neuroma acústico
title_short Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
title_full Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
title_fullStr Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
title_full_unstemmed Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
title_sort Neurosurgical Management of a Giant Parasagittal Meningioma in a Patient with Neurofibromatosis Type 2: A Case Report
dc.creator.none.fl_str_mv Aguilar, Luis
Váscones-Román , Fritz Fidel
Caucha Morales , Yelimer
author Aguilar, Luis
author_facet Aguilar, Luis
Váscones-Román , Fritz Fidel
Caucha Morales , Yelimer
author_role author
author2 Váscones-Román , Fritz Fidel
Caucha Morales , Yelimer
author2_role author
author
dc.subject.none.fl_str_mv Neurofibromatosis 2
Meningioma
Brain neoplasms
Neurofibromatosis 2
meningioma
neuroma acústico
topic Neurofibromatosis 2
Meningioma
Brain neoplasms
Neurofibromatosis 2
meningioma
neuroma acústico
description Parasagittal meningiomas are intracranial tumors that develop along the superior sagittal sinus. Although they are generally benign, their proximity to vital vascular structures poses significant challenges for surgical management. In patients with neurofibromatosis type 2 (NF2), an autosomal dominant genetic disorder, there is a high predisposition to develop multiple tumors in the central nervous system, including meningiomas and schwannomas. The report discusses a 23-year-old woman with a family history of NF2 who presented with a large parasagittal meningioma and bilateral schwannomas, along with symptoms such as headaches, hearing loss, vertigo, and seizures. MRI revealed a right frontoparietal meningioma invading the superior sagittal sinus. Successful craniotomy and resection showed a poorly vascularized meningioma invading the sagittal sinus. This case highlights the surgical difficulties associated with sagittal sinus meningioma invasion and emphasizes the importance of multidisciplinary care and long-term follow-up due to the high risk of tumor recurrence in NF2 patients.
publishDate 2025
dc.date.none.fl_str_mv 2025-09-30
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed article
Artículo evaluado por pares
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://revistas.upch.edu.pe/index.php/RMH/article/view/5841
10.20453/rmh.v36i3.5841
url https://revistas.upch.edu.pe/index.php/RMH/article/view/5841
identifier_str_mv 10.20453/rmh.v36i3.5841
dc.language.none.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://revistas.upch.edu.pe/index.php/RMH/article/view/5841/6692
dc.rights.none.fl_str_mv Derechos de autor 2025 Luis Aguilar, Fritz Vascones, Yelimer Caucha
http://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Derechos de autor 2025 Luis Aguilar, Fritz Vascones, Yelimer Caucha
http://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
dc.source.none.fl_str_mv Revista Médica Herediana; Vol. 36 No. 3 (2025): Julio-septiembre; 247-251
Revista Médica Herediana; Vol. 36 Núm. 3 (2025): Julio-septiembre; 247-251
Revista Medica Herediana; v. 36 n. 3 (2025): Julio-septiembre; 247-251
1729-214X
1018-130X
10.20453/rmh.v36i3
reponame:Revistas - Universidad Peruana Cayetano Heredia
instname:Universidad Peruana Cayetano Heredia
instacron:UPCH
instname_str Universidad Peruana Cayetano Heredia
instacron_str UPCH
institution UPCH
reponame_str Revistas - Universidad Peruana Cayetano Heredia
collection Revistas - Universidad Peruana Cayetano Heredia
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