Proximal type epithelioid sarcoma of the vulva

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Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioidsarcoma of the vulva is an extremely rare malignant tumor of the soft tissues withfrequent recurrences due to its aggressive behaviour. Because its characteristicsare similar to other benign lesions, this leads to diag...

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Detalles Bibliográficos
Autores: Torres-Cepeda, Duly, Rondon-Tapia, Martha, Reyna-Villasmil, Eduardo
Formato: artículo
Fecha de Publicación:2022
Institución:Sociedad Peruana de Obstetricia y Ginecología
Repositorio:Revista Peruana de Ginecología y Obstetricia
Lenguaje:español
inglés
OAI Identifier:oai:ginecologiayobstetricia.pe:article/2420
Enlace del recurso:https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420
Nivel de acceso:acceso abierto
Materia:Vulva
Sarcoma epitelioide
Neoplasia de la vulva
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spelling Proximal type epithelioid sarcoma of the vulvaSarcoma epitelioide de tipo proximal de vulvaTorres-Cepeda, DulyRondon-Tapia, MarthaReyna-Villasmil, EduardoVulvaSarcoma epitelioideNeoplasia de la vulvaEpithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioidsarcoma of the vulva is an extremely rare malignant tumor of the soft tissues withfrequent recurrences due to its aggressive behaviour. Because its characteristicsare similar to other benign lesions, this leads to diagnostic and therapeutic delays.Histologic features of this tumor include prominent epithelioid cells and theappearance of rhabdoid features with marked nuclear atypia. Due to its low incidence,there are no evidence-based diagnostic algorithms or published recommendationsfor treatment. The prognosis is generally poor. A case of proximal type epithelioidsarcoma of the vulva is presented.El sarcoma epitelioide es un tipo raro de tumor mesenquimal. El sarcoma epitelioide de tipo proximal de vulva es un tumor maligno extremadamente raro de los tejidos blandos, con frecuentes recurrencias por su comportamiento agresivo. Debido a que sus características son similares a otras lesiones benignas, esto lleva a retrasos diagnósticos y terapéuticos. Las características histológicas de este tumor incluyen células epitelioides prominentes y aparición de rasgos rabdoides con marcadas atipias nucleares. Debido a su baja incidencia, no existen algoritmos diagnósticos basados en la evidencia ni recomendaciones publicadas para el tratamiento. El pronóstico es generalmente malo. Se presenta un caso de sarcoma epitelioide de tipo proximal de vulva.Sociedad Peruana de Obstetricia y Ginecología2022-07-06info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfapplication/pdfhttps://ginecologiayobstetricia.pe/index.php/RPGO/article/view/242010.31403/rpgo.v68i2420The Peruvian Journal of Gynecology and Obstetrics ; Vol. 68 No. 2 (2022)Revista Peruana de Ginecología y Obstetricia; Vol. 68 Núm. 2 (2022)2304-51322304-5124reponame:Revista Peruana de Ginecología y Obstetriciainstname:Sociedad Peruana de Obstetricia y Ginecologíainstacron:SPOGspaenghttps://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420/2621https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420/2622Derechos de autor 2022 Duly Torres-Cepeda, Martha Rondon-Tapia, Eduardo Reyna-Villasmilhttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessoai:ginecologiayobstetricia.pe:article/24202026-01-12T15:22:08Z
dc.title.none.fl_str_mv Proximal type epithelioid sarcoma of the vulva
Sarcoma epitelioide de tipo proximal de vulva
title Proximal type epithelioid sarcoma of the vulva
spellingShingle Proximal type epithelioid sarcoma of the vulva
Torres-Cepeda, Duly
Vulva
Sarcoma epitelioide
Neoplasia de la vulva
title_short Proximal type epithelioid sarcoma of the vulva
title_full Proximal type epithelioid sarcoma of the vulva
title_fullStr Proximal type epithelioid sarcoma of the vulva
title_full_unstemmed Proximal type epithelioid sarcoma of the vulva
title_sort Proximal type epithelioid sarcoma of the vulva
dc.creator.none.fl_str_mv Torres-Cepeda, Duly
Rondon-Tapia, Martha
Reyna-Villasmil, Eduardo
author Torres-Cepeda, Duly
author_facet Torres-Cepeda, Duly
Rondon-Tapia, Martha
Reyna-Villasmil, Eduardo
author_role author
author2 Rondon-Tapia, Martha
Reyna-Villasmil, Eduardo
author2_role author
author
dc.subject.none.fl_str_mv Vulva
Sarcoma epitelioide
Neoplasia de la vulva
topic Vulva
Sarcoma epitelioide
Neoplasia de la vulva
description Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioidsarcoma of the vulva is an extremely rare malignant tumor of the soft tissues withfrequent recurrences due to its aggressive behaviour. Because its characteristicsare similar to other benign lesions, this leads to diagnostic and therapeutic delays.Histologic features of this tumor include prominent epithelioid cells and theappearance of rhabdoid features with marked nuclear atypia. Due to its low incidence,there are no evidence-based diagnostic algorithms or published recommendationsfor treatment. The prognosis is generally poor. A case of proximal type epithelioidsarcoma of the vulva is presented.
publishDate 2022
dc.date.none.fl_str_mv 2022-07-06
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420
10.31403/rpgo.v68i2420
url https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420
identifier_str_mv 10.31403/rpgo.v68i2420
dc.language.none.fl_str_mv spa
eng
language spa
eng
dc.relation.none.fl_str_mv https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420/2621
https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2420/2622
dc.rights.none.fl_str_mv Derechos de autor 2022 Duly Torres-Cepeda, Martha Rondon-Tapia, Eduardo Reyna-Villasmil
https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Derechos de autor 2022 Duly Torres-Cepeda, Martha Rondon-Tapia, Eduardo Reyna-Villasmil
https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv Sociedad Peruana de Obstetricia y Ginecología
publisher.none.fl_str_mv Sociedad Peruana de Obstetricia y Ginecología
dc.source.none.fl_str_mv The Peruvian Journal of Gynecology and Obstetrics ; Vol. 68 No. 2 (2022)
Revista Peruana de Ginecología y Obstetricia; Vol. 68 Núm. 2 (2022)
2304-5132
2304-5124
reponame:Revista Peruana de Ginecología y Obstetricia
instname:Sociedad Peruana de Obstetricia y Ginecología
instacron:SPOG
instname_str Sociedad Peruana de Obstetricia y Ginecología
instacron_str SPOG
institution SPOG
reponame_str Revista Peruana de Ginecología y Obstetricia
collection Revista Peruana de Ginecología y Obstetricia
repository.name.fl_str_mv
repository.mail.fl_str_mv
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score 13.47265
Proximal type epithelioid sarcoma of the vulva
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