Prenatal diagnosis of fetal hepatic mesenchymal hamartoma

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Fetal primary liver tumors are rare. Hepatic mesenchymal hamartoma is a rare benigntumor. It is the second most common primary liver tumors after hepatoblastomaand is composed of an abnormal mixture of liver tissue cells of uncertain etiology.It usually appears as a rapidly growing cystic abdominal...

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Detalles Bibliográficos
Autores: Reyna-Villasmil, Eduardo, Rondon-Tapia, Martha, Torres-Cepeda, Duly
Formato: artículo
Fecha de Publicación:2022
Institución:Sociedad Peruana de Obstetricia y Ginecología
Repositorio:Revista Peruana de Ginecología y Obstetricia
Lenguaje:español
inglés
OAI Identifier:oai:ginecologiayobstetricia.pe:article/2457
Enlace del recurso:https://ginecologiayobstetricia.pe/index.php/RPGO/article/view/2457
Nivel de acceso:acceso abierto
Materia:Liver
Hamartoma
mesenchymal
Prenatal diagnosis
Fetus
Hamartoma mesenquimatoso hepático
Diagnóstico prenatal
Feto
Descripción
Sumario:Fetal primary liver tumors are rare. Hepatic mesenchymal hamartoma is a rare benigntumor. It is the second most common primary liver tumors after hepatoblastomaand is composed of an abnormal mixture of liver tissue cells of uncertain etiology.It usually appears as a rapidly growing cystic abdominal tumor that occupies spaceand can potentially compress adjacent organs, resulting in various complications,including death. Prenatal diagnosis is challenging. Histopathologically, it presentswith variable myxomatous mesenchymal proliferation and malformed bile ducts.Although histologically benign, this lesion often results in perinatal complications.It can be life-threatening in the prenatal or neonatal period and the prognosticsignificance of prenatal detection is still unknown. A case of prenatal diagnosis offetal hepatic mesenchymal hamartoma is presented.
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