Hemoperitoneum secondary to a malignant tumor of the sheath of the peripheral nerve in the liver

• Autores: Chávez-Sánchez, Siomara Aransuzú, Bellido-Caparó, Álvaro, Gallegos-Serruto, Guido Saúl, Vásquez Morales, Víctor Manuel, Bravo-Taxa, Mercedes Del Pilar, García-Encinas, Carlos Aurelio
• Formato: artículo
• Fecha de Publicación: 2024
• Institución: Sociedad de Gastroenterología del Perú
• Repositorio: Revista de Gastroenterología del Perú
• Lenguaje: español
• OAI Identifier: oai:ojs.revistagastroperu.com:article/1701
• Enlace del recurso: https://revistagastroperu.com/index.php/rgp/article/view/1701
• Nivel de acceso: acceso abierto
• Materia: Tumor maligno; Tumor de la vaina del nervio periférico; Neurofibromatosis; Hígado; Hemoperitoneo; Neoplasm, malignant; Peripheral nerve sheath tumor; Neurofibromatoses; Liver; Hemoperitoneum

Malignant peripheral nerve sheath tumors are frequently associated with neurofibromatosis type 1. They are usually located in the extremities or in the axial area. Its visceral location is very rare and its hepatic origin is infrequent. They tend to be aggressive with a poor response to chemotherapy and radiotherapy, so surgical management is the best treatment option. We present the case of a young man with neurofibromatosis type 1, who presented with hemoperitoneum as a complication of a malignant tumor of the peripheral nerve sheath located in the liver.