Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia

Descripción del Articulo

We report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorect...

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Detalles Bibliográficos
Autores: Guerrero Arismendiz, Bruno Renato, Javier-Najarro, Rosario, Díaz-Torres, Carlos, Peñaloza-Maquera, Saul, Cornejo-Salazar, Jose Luis
Formato: artículo
Fecha de Publicación:2023
Institución:Colegio Médico del Perú
Repositorio:Acta Médica Peruana
Lenguaje:inglés
OAI Identifier:oai:ojs.pkp.sfu.ca:article/2580
Enlace del recurso:https://amp.cmp.org.pe/index.php/AMP/article/view/2580
Nivel de acceso:acceso abierto
Materia:Glanzmann's thrombasthenia
Recombinant factor VII
Hysterectomy
Peru
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spelling Successful outcomes of surgery procedures in patient with Glanzmann´s ThrombastheniaResultados exitosos de procedimientos quirúrgicos en paciente con trombastenia de GlanzmannGuerrero Arismendiz, Bruno RenatoJavier-Najarro, RosarioDíaz-Torres, CarlosPeñaloza-Maquera, SaulCornejo-Salazar, Jose LuisGlanzmann's thrombastheniaRecombinant factor VIIHysterectomyPeruWe report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorectomy was proposed and recombinant factor VII was required. Surgical and postoperative outcomes were successful, without surgical complications, bleeding, or hemogram alterations. 4 years later, she required tooth extraction because of periodontal disease and pulp necrosis. In Peru, reports of GT patients requiring major and minor surgical procedures are lacking, given the low disease prevalence and the difficulties related to surgery. The report of these successful cases becomes relevant to continue improving GT management.Presentamos el caso de una paciente de 35 años con trombastenia de Glanzmann (GT) y anemia severa por sangrado uterino anormal secundario a miomatosis uterina. Requirió varias admisiones de transfusiones de glóbulos rojos y plaquetas. Se propuso histerectomía subtotal electiva con salpingooforectomía y se requirió factor VII recombinante. Los resultados quirúrgicos y postoperatorios fueron exitosos, sin complicaciones quirúrgicas, sangrado ni alteraciones del hemograma. 4 años después, requirió extracción dental por enfermedad periodontal y necrosis pulpar. En Perú son escasos los reportes de pacientes con GT que requieren procedimientos quirúrgicos mayores y menores, dada la baja prevalencia de la enfermedad y las dificultades relacionadas con la cirugía. El reporte de estos casos de éxito cobra relevancia para seguir mejorando la gestión de GT.Colegio Médico del Perú2023-07-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://amp.cmp.org.pe/index.php/AMP/article/view/258010.35663/amp.2023.402.2580ACTA MEDICA PERUANA; Vol 40 No 2 (2023): April - JuneACTA MEDICA PERUANA; Vol. 40 Núm. 2 (2023): Abril - Junio1728-59171018-8800reponame:Acta Médica Peruanainstname:Colegio Médico del Perúinstacron:CMPenghttps://amp.cmp.org.pe/index.php/AMP/article/view/2580/1562Copyright (c) 2023 ACTA MEDICA PERUANAinfo:eu-repo/semantics/openAccessoai:ojs.pkp.sfu.ca:article/25802024-03-21T00:09:28Z
dc.title.none.fl_str_mv Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
Resultados exitosos de procedimientos quirúrgicos en paciente con trombastenia de Glanzmann
title Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
spellingShingle Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
Guerrero Arismendiz, Bruno Renato
Glanzmann's thrombasthenia
Recombinant factor VII
Hysterectomy
Peru
title_short Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
title_full Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
title_fullStr Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
title_full_unstemmed Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
title_sort Successful outcomes of surgery procedures in patient with Glanzmann´s Thrombasthenia
dc.creator.none.fl_str_mv Guerrero Arismendiz, Bruno Renato
Javier-Najarro, Rosario
Díaz-Torres, Carlos
Peñaloza-Maquera, Saul
Cornejo-Salazar, Jose Luis
author Guerrero Arismendiz, Bruno Renato
author_facet Guerrero Arismendiz, Bruno Renato
Javier-Najarro, Rosario
Díaz-Torres, Carlos
Peñaloza-Maquera, Saul
Cornejo-Salazar, Jose Luis
author_role author
author2 Javier-Najarro, Rosario
Díaz-Torres, Carlos
Peñaloza-Maquera, Saul
Cornejo-Salazar, Jose Luis
author2_role author
author
author
author
dc.subject.none.fl_str_mv Glanzmann's thrombasthenia
Recombinant factor VII
Hysterectomy
Peru
topic Glanzmann's thrombasthenia
Recombinant factor VII
Hysterectomy
Peru
description We report a 35-year-old female patient with Glanzmann's thrombasthenia (GT) and severe anemia due to abnormal uterine bleeding secondary to uterine myomatosis. She required several admissions of red blood cells and platelet transfusions. An elective subtotal hysterectomy with salpingo-oophorectomy was proposed and recombinant factor VII was required. Surgical and postoperative outcomes were successful, without surgical complications, bleeding, or hemogram alterations. 4 years later, she required tooth extraction because of periodontal disease and pulp necrosis. In Peru, reports of GT patients requiring major and minor surgical procedures are lacking, given the low disease prevalence and the difficulties related to surgery. The report of these successful cases becomes relevant to continue improving GT management.
publishDate 2023
dc.date.none.fl_str_mv 2023-07-31
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://amp.cmp.org.pe/index.php/AMP/article/view/2580
10.35663/amp.2023.402.2580
url https://amp.cmp.org.pe/index.php/AMP/article/view/2580
identifier_str_mv 10.35663/amp.2023.402.2580
dc.language.none.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://amp.cmp.org.pe/index.php/AMP/article/view/2580/1562
dc.rights.none.fl_str_mv Copyright (c) 2023 ACTA MEDICA PERUANA
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2023 ACTA MEDICA PERUANA
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Colegio Médico del Perú
publisher.none.fl_str_mv Colegio Médico del Perú
dc.source.none.fl_str_mv ACTA MEDICA PERUANA; Vol 40 No 2 (2023): April - June
ACTA MEDICA PERUANA; Vol. 40 Núm. 2 (2023): Abril - Junio
1728-5917
1018-8800
reponame:Acta Médica Peruana
instname:Colegio Médico del Perú
instacron:CMP
instname_str Colegio Médico del Perú
instacron_str CMP
institution CMP
reponame_str Acta Médica Peruana
collection Acta Médica Peruana
repository.name.fl_str_mv
repository.mail.fl_str_mv
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