Splenic lymphangiomatosis in an adult patient Case report
Descripción del Articulo
Lymphangiomas are benign malformations of the lymphatic system. They most often affect children and rarely adults. We present the case of a 36-year-old woman with a 6-month clinical picture of diffuse abdominal pain without peritoneal irritation associated with adynamia. As part of the studies, a co...
Autores: | , , , , |
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Formato: | artículo |
Fecha de Publicación: | 2022 |
Institución: | Colegio Médico del Perú |
Repositorio: | Acta Médica Peruana |
Lenguaje: | español |
OAI Identifier: | oai:ojs.pkp.sfu.ca:article/2451 |
Enlace del recurso: | https://amp.cmp.org.pe/index.php/AMP/article/view/2451 |
Nivel de acceso: | acceso abierto |
Materia: | Anomalies Benign Neoplasm Lymphangioma Splenic Neoplasms |
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Splenic lymphangiomatosis in an adult patient Case reportLinfangiomatosis esplénica en un paciente adulto, Reporte de casoJiménez-Canizales, Carlos Eduardo Bolaños, Fernando Benavides-López, Ernesto Federico Mondragón-Cardona, Álvaro Eduardo Rojas-Gómez, Oscar Fabián AnomaliesBenign NeoplasmLymphangiomaSplenic NeoplasmsLymphangiomas are benign malformations of the lymphatic system. They most often affect children and rarely adults. We present the case of a 36-year-old woman with a 6-month clinical picture of diffuse abdominal pain without peritoneal irritation associated with adynamia. As part of the studies, a computerized axial tomography with abdominal contrast was requested, which revealed multiple hypovascular hypodense splenic lesions with suspected diagnosis of lymphoproliferative lesions. For this reason, a diagnostic splenectomy was requested, which showed macroscopic, microscopic and immunohistochemical findings (positivity of cystic lesions for CD31 and D2-40) compatible with diffuse splenic lymphagiomatosis.Los linfangiomas son malformaciones benignas del sistema linfático que afectan con mayor frecuencia a los niños y en raras ocasiones a adultos. Presentamos el caso de una mujer de 36 años, con cuadro clínico de 6 meses de dolor abdominal difuso sin irritación peritoneal, y asociado a adinamia. Como parte de los estudios, se solicitó una tomografía axial computarizada con contraste de abdomen, que reveló múltiples lesiones esplénicas hipodensas hipovasculares, con sospecha diagnóstica de lesiones linfoproliferativas. Por tal motivo se solicitó una esplenectomía diagnóstica, que finalmente mostró hallazgos macroscópicos, microscópicos y de inmunohistoquímica (positividad de las lesiones quísticas para CD31 y D2-40) compatibles con linfagiomatosis esplénica difusa.Colegio Médico del Perú2022-12-06info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://amp.cmp.org.pe/index.php/AMP/article/view/245110.35663/amp.2022.394.2451ACTA MEDICA PERUANA; Vol 39 No 4 (2022): October - DecemberACTA MEDICA PERUANA; Vol. 39 Núm. 4 (2022): Octubre - Diciembre1728-59171018-8800reponame:Acta Médica Peruanainstname:Colegio Médico del Perúinstacron:CMPspahttps://amp.cmp.org.pe/index.php/AMP/article/view/2451/1490Copyright (c) 2022 ACTA MEDICA PERUANAinfo:eu-repo/semantics/openAccessoai:ojs.pkp.sfu.ca:article/24512023-07-01T03:26:00Z |
dc.title.none.fl_str_mv |
Splenic lymphangiomatosis in an adult patient Case report Linfangiomatosis esplénica en un paciente adulto, Reporte de caso |
title |
Splenic lymphangiomatosis in an adult patient Case report |
spellingShingle |
Splenic lymphangiomatosis in an adult patient Case report Jiménez-Canizales, Carlos Eduardo Anomalies Benign Neoplasm Lymphangioma Splenic Neoplasms |
title_short |
Splenic lymphangiomatosis in an adult patient Case report |
title_full |
Splenic lymphangiomatosis in an adult patient Case report |
title_fullStr |
Splenic lymphangiomatosis in an adult patient Case report |
title_full_unstemmed |
Splenic lymphangiomatosis in an adult patient Case report |
title_sort |
Splenic lymphangiomatosis in an adult patient Case report |
dc.creator.none.fl_str_mv |
Jiménez-Canizales, Carlos Eduardo Bolaños, Fernando Benavides-López, Ernesto Federico Mondragón-Cardona, Álvaro Eduardo Rojas-Gómez, Oscar Fabián |
author |
Jiménez-Canizales, Carlos Eduardo |
author_facet |
Jiménez-Canizales, Carlos Eduardo Bolaños, Fernando Benavides-López, Ernesto Federico Mondragón-Cardona, Álvaro Eduardo Rojas-Gómez, Oscar Fabián |
author_role |
author |
author2 |
Bolaños, Fernando Benavides-López, Ernesto Federico Mondragón-Cardona, Álvaro Eduardo Rojas-Gómez, Oscar Fabián |
author2_role |
author author author author |
dc.subject.none.fl_str_mv |
Anomalies Benign Neoplasm Lymphangioma Splenic Neoplasms |
topic |
Anomalies Benign Neoplasm Lymphangioma Splenic Neoplasms |
description |
Lymphangiomas are benign malformations of the lymphatic system. They most often affect children and rarely adults. We present the case of a 36-year-old woman with a 6-month clinical picture of diffuse abdominal pain without peritoneal irritation associated with adynamia. As part of the studies, a computerized axial tomography with abdominal contrast was requested, which revealed multiple hypovascular hypodense splenic lesions with suspected diagnosis of lymphoproliferative lesions. For this reason, a diagnostic splenectomy was requested, which showed macroscopic, microscopic and immunohistochemical findings (positivity of cystic lesions for CD31 and D2-40) compatible with diffuse splenic lymphagiomatosis. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-12-06 |
dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.none.fl_str_mv |
https://amp.cmp.org.pe/index.php/AMP/article/view/2451 10.35663/amp.2022.394.2451 |
url |
https://amp.cmp.org.pe/index.php/AMP/article/view/2451 |
identifier_str_mv |
10.35663/amp.2022.394.2451 |
dc.language.none.fl_str_mv |
spa |
language |
spa |
dc.relation.none.fl_str_mv |
https://amp.cmp.org.pe/index.php/AMP/article/view/2451/1490 |
dc.rights.none.fl_str_mv |
Copyright (c) 2022 ACTA MEDICA PERUANA info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
Copyright (c) 2022 ACTA MEDICA PERUANA |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Colegio Médico del Perú |
publisher.none.fl_str_mv |
Colegio Médico del Perú |
dc.source.none.fl_str_mv |
ACTA MEDICA PERUANA; Vol 39 No 4 (2022): October - December ACTA MEDICA PERUANA; Vol. 39 Núm. 4 (2022): Octubre - Diciembre 1728-5917 1018-8800 reponame:Acta Médica Peruana instname:Colegio Médico del Perú instacron:CMP |
instname_str |
Colegio Médico del Perú |
instacron_str |
CMP |
institution |
CMP |
reponame_str |
Acta Médica Peruana |
collection |
Acta Médica Peruana |
repository.name.fl_str_mv |
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repository.mail.fl_str_mv |
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1816075112040890368 |
score |
13.7211075 |
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La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).