Herlyn-Werner-Wünderlich syndrome with late diagnosis: a propos of a case

• Autores: Boria Alegre, Félix, Lucas Ramos, Javier, Álvarez-López, Covadonga, Poza Cordón, Joaquín
• Formato: artículo
• Fecha de Publicación: 2019
• Institución: Sociedad Peruana de Obstetricia y Ginecología
• Repositorio: Revista SPOG - Revista Peruana de Ginecología y Obstetricia
• Lenguaje: español
• OAI Identifier: oai:ojs.spog:article/2191
• Enlace del recurso: http://www.spog.org.pe/web/revista/index.php/RPGO/article/view/2191
• Nivel de acceso: acceso abierto

Herlyn-Werner-Wünderlich syndrome is a rare congenital anomaly that affects the genitourinary system. It is defined by the triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It consists in a Mullerian anomaly. Most patients remain asymptomatic until the menarche, when they present dysmenorrhea, pelvic pain, and a pelvic mass is noticed due to hematocolpos. We present the case of a 32-year-old patient studied for infertility. 3D transvaginal ultrasound and hysterosalpingography showed uterus didelphys and a blind hemivagina. Speculoscopy during menses revealed a normal cervix and a little orifice on the lateral vagina where blood could be seen draining from a fistulized hemivagina. The abdominal ultrasound showed ipsilateral renal agenesis, confirming the suspected diagnosis.