Introduction In the hypermobile Ehlers-Danlos syndrome (EDSht) there is an important frequency of cardiovascular symptoms. Studies have been conducted in patients diagnosed with Brighton criteria. The objective of this research was to determine the frequency of echocardiographic symptoms and abnormalities in the unselected adult population, diagnosed with EDSht, in a cardiology office, with the criteria of the International Classification of Ehlers-Danlos syndromes, published in 2017. Methods The descriptive study in patients diagnosed with EDSht was employed, older than 12 years, attended in an outpatient clinic of cardiology of San Salvador, El Salvador, between 2012 and 2019. Clinical history, physical examination, anthropometry, the Beighton score was employed, 10-minute postural test and echocardiography (ECHO) findings were recorded. Results The EDSht was diagnosed in 57 patients, ...

Introduction In the hypermobile Ehlers-Danlos syndrome (EDSht) there is an important frequency of cardiovascular symptoms. Studies have been conducted in patients diagnosed with Brighton criteria. The objective of this research was to determine the frequency of echocardiographic symptoms and abnormalities in the unselected adult population, diagnosed with EDSht, in a cardiology office, with the criteria of the International Classification of Ehlers-Danlos syndromes, published in 2017. Methods The descriptive study in patients diagnosed with EDSht was employed, older than 12 years, attended in an outpatient clinic of cardiology of San Salvador, El Salvador, between 2012 and 2019. Clinical history, physical examination, anthropometry, the Beighton score was employed, 10-minute postural test and echocardiography (ECHO) findings were recorded. Results The EDSht was diagnosed in 57 patients, ...