Diastematomyelia is a congenital disorder characterized by a division of the spinal cord separated by a fibrous or bony septum. When related to scoliosis, this condition may lead to neurological symptoms depending on its location and severity, such as back pain, leg weakness or paralysis, and sphincter disorders. Surgical treatment involves exploring and releasing the fibrous or bone tissue that causes the separation of the spinal cord through a laminectomy, prior to corrective scoliosis surgery. We present this clinical case report consisting of diastematomyelia associated with congenital scoliosis with the objective of analyzing the symptoms at presentation, and to evaluate the effectiveness of the surgical procedure and discuss the clinical results obtained. The idea is to contribute to better understanding the management of these interrelated conditions and their impact on t...