Intralobar bronchopulmonary sequestration consists of isolated non- functioning lung tissue that lacks normal communication to the tracheobronchial tree. It has systemic arterial supply and venous drainage to the pulmonary veins or the left atrium. Whereas extralobar sequestration is clearly congenital, intralobar sequestration may have a congenital or acquired origin and frequently presents in older children (usually older than 10 years old). We present the case of a 3 years old patient with recurrent attacks of basal right lung pneumonia. Intralobar pulmonary sequestration was confirmed by arteriogram. We must consider this lesion among the diagnostic approach to children with clinical and radiological findings suggestive of pneumonia and poor response to the administered antibiotics. The usefulness of different imaging techniques for the diagnosis is also addressed.