Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report

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Hypohydrotic ectodermal dysplasia (HED) is a genetic disorder that affects the development of ectodermal tissues. This study reports a case of a 5-year-old male patient, with clinical extra and intraoral characteristics of HED. The intraoral clinical examination revealed a generalized absence of tee...

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Detalles Bibliográficos
Autor: Sánchez-Tito, Marco A.
Formato: artículo
Fecha de Publicación:2022
Institución:Universidad Peruana Cayetano Heredia
Repositorio:Revistas - Universidad Peruana Cayetano Heredia
Lenguaje:español
OAI Identifier:oai:revistas.upch.edu.pe:article/4186
Enlace del recurso:https://revistas.upch.edu.pe/index.php/REH/article/view/4186
Nivel de acceso:acceso abierto
Materia:Displasia ectodérmica hipohidrótica
cefalometría
desarrollo maxilofacial
Hypohidrotic ectodermal dysplasia
cephalometry
maxillofacial development
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network_name_str Revistas - Universidad Peruana Cayetano Heredia
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spelling Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case reportOral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case reportSánchez-Tito, Marco A.Displasia ectodérmica hipohidróticacefalometríadesarrollo maxilofacialHypohidrotic ectodermal dysplasiacephalometrymaxillofacial developmentHypohydrotic ectodermal dysplasia (HED) is a genetic disorder that affects the development of ectodermal tissues. This study reports a case of a 5-year-old male patient, with clinical extra and intraoral characteristics of HED. The intraoral clinical examination revealed a generalized absence of teeth, panoramic radiograph revealed the presence of permanent first molars with taurodontism, and confirm the oligodontia. Cephalometric analysis revealed a class III skeletal relationship, due to deficiency in the sagittal development of the maxilla and an anti-clockwise growth tendency. Alterations in craniofacial development require multidisciplinary treatment and long-term follow-up to monitor craniofacial growth.Hypohydrotic ectodermal dysplasia (HED) is a genetic disorder that affects the development of ectodermal tissues. This study reports a case of a 5-year-old male patient, with clinical extra and intraoral characteristics of HED. The intraoral clinical examination revealed a generalized absence of teeth, panoramic radiograph revealed the presence of permanent first molars with taurodontism, and confirm the oligodontia. Cephalometric analysis revealed a class III skeletal relationship, due to deficiency in the sagittal development of the maxilla and an anti-clockwise growth tendency. Alterations in craniofacial development require multidisciplinary treatment and long-term follow-up to monitor craniofacial growth.Universidad Peruana Cayetano Heredia2022-04-22info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://revistas.upch.edu.pe/index.php/REH/article/view/418610.20453/reh.v32i1.4186Revista Estomatológica Herediana; Vol. 32 No. 1 (2022): January-March; 74-78Revista Estomatológica Herediana; Vol. 32 Núm. 1 (2022): Enero-Marzo; 74-78Revista Estomatológica Herediana; v. 32 n. 1 (2022): Enero-Marzo; 74-782225-76161019-4355reponame:Revistas - Universidad Peruana Cayetano Herediainstname:Universidad Peruana Cayetano Herediainstacron:UPCHspahttps://revistas.upch.edu.pe/index.php/REH/article/view/4186/4740Derechos de autor 2022 Marco A. Sánchez-Titoinfo:eu-repo/semantics/openAccessoai:revistas.upch.edu.pe:article/41862023-08-21T19:56:57Z
dc.title.none.fl_str_mv Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
title Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
spellingShingle Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
Sánchez-Tito, Marco A.
Displasia ectodérmica hipohidrótica
cefalometría
desarrollo maxilofacial
Hypohidrotic ectodermal dysplasia
cephalometry
maxillofacial development
title_short Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
title_full Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
title_fullStr Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
title_full_unstemmed Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
title_sort Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
dc.creator.none.fl_str_mv Sánchez-Tito, Marco A.
author Sánchez-Tito, Marco A.
author_facet Sánchez-Tito, Marco A.
author_role author
dc.subject.none.fl_str_mv Displasia ectodérmica hipohidrótica
cefalometría
desarrollo maxilofacial
Hypohidrotic ectodermal dysplasia
cephalometry
maxillofacial development
topic Displasia ectodérmica hipohidrótica
cefalometría
desarrollo maxilofacial
Hypohidrotic ectodermal dysplasia
cephalometry
maxillofacial development
description Hypohydrotic ectodermal dysplasia (HED) is a genetic disorder that affects the development of ectodermal tissues. This study reports a case of a 5-year-old male patient, with clinical extra and intraoral characteristics of HED. The intraoral clinical examination revealed a generalized absence of teeth, panoramic radiograph revealed the presence of permanent first molars with taurodontism, and confirm the oligodontia. Cephalometric analysis revealed a class III skeletal relationship, due to deficiency in the sagittal development of the maxilla and an anti-clockwise growth tendency. Alterations in craniofacial development require multidisciplinary treatment and long-term follow-up to monitor craniofacial growth.
publishDate 2022
dc.date.none.fl_str_mv 2022-04-22
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://revistas.upch.edu.pe/index.php/REH/article/view/4186
10.20453/reh.v32i1.4186
url https://revistas.upch.edu.pe/index.php/REH/article/view/4186
identifier_str_mv 10.20453/reh.v32i1.4186
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv https://revistas.upch.edu.pe/index.php/REH/article/view/4186/4740
dc.rights.none.fl_str_mv Derechos de autor 2022 Marco A. Sánchez-Tito
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Derechos de autor 2022 Marco A. Sánchez-Tito
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
publisher.none.fl_str_mv Universidad Peruana Cayetano Heredia
dc.source.none.fl_str_mv Revista Estomatológica Herediana; Vol. 32 No. 1 (2022): January-March; 74-78
Revista Estomatológica Herediana; Vol. 32 Núm. 1 (2022): Enero-Marzo; 74-78
Revista Estomatológica Herediana; v. 32 n. 1 (2022): Enero-Marzo; 74-78
2225-7616
1019-4355
reponame:Revistas - Universidad Peruana Cayetano Heredia
instname:Universidad Peruana Cayetano Heredia
instacron:UPCH
instname_str Universidad Peruana Cayetano Heredia
instacron_str UPCH
institution UPCH
reponame_str Revistas - Universidad Peruana Cayetano Heredia
collection Revistas - Universidad Peruana Cayetano Heredia
repository.name.fl_str_mv
repository.mail.fl_str_mv
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Oral and cephalometric characteristics of hypohidrotic ectodermal dysplasia: Case report
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