Enfermedad poliquística hepatorrenal complicada con suboclusión intestinal: Reporte de un caso.: Hepatorenal polychistic disease complicated with intestinal suboclusion: A case report.

• Autores: Salinas Calderón, Jonathan Alexander, Salinas Calderón, Stephany Lizbeth, Vargas Quiroz, Albert Christopher, Mozo Marquina, Renzzo Amaro, Leon Risco, Anthony Omar, Leon Risco, Kevyn Bryce, Velásquez Ojeda, Celso Anghelo
• Formato: artículo
• Fecha de Publicación: 2022
• Institución: Universidad Nacional de Trujillo
• Repositorio: Revistas - Universidad Nacional de Trujillo
• Lenguaje: español
• OAI Identifier: oai:ojs.revistas.unitru.edu.pe:article/4218
• Enlace del recurso: https://revistas.unitru.edu.pe/index.php/RMT/article/view/4218
• Nivel de acceso: acceso abierto
• Materia: polycystic liver-renal disease; intestinal subocclusion; cysts; liver; kidney; enfermedad poliquística hepática-renal; suboclusión intestinal; quistes; hígado; riñón

Autosomal Dominant Polycystic Kidney Disease, known by its acronym ADPKD (Autosomal Dominant Polycystic kidney disease), is a condition of genetic origin characterized by two types of mutations in the PKD1 and PKD2 genes that code for polycystins (PC) 1 and 2, respectively. It is associated with extrarenal manifestations, both cystic and non-cystic; the liver is the most affected organ within the cystic manifestations; as well as cerebral vascular alterations, in non-cystic ones. We report a 44-year-old woman with polycystic hepato-renal disease (PLKD) complicated by intestinal subocclusion.