Evans syndrome and primary biliary cholangitis: A case report
Descripción del Articulo
In this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagno...
Autores: | , , , , , , |
---|---|
Formato: | artículo |
Fecha de Publicación: | 2024 |
Institución: | Universidad Nacional de Trujillo |
Repositorio: | Revistas - Universidad Nacional de Trujillo |
Lenguaje: | español |
OAI Identifier: | oai:ojs.revistas.unitru.edu.pe:article/6190 |
Enlace del recurso: | https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190 |
Nivel de acceso: | acceso abierto |
Materia: | anemia hemolítica autoinmune púrpura trombocitopénica idiopática cirrosis biliar primaria colecistitis autoimmune hemolytic anemia idiopathic thrombocytopenic purpura primary biliary cirrhosis cholecystitis |
id |
REVUNITRU_95b3616833a1f319efcbd06e4fd5586d |
---|---|
oai_identifier_str |
oai:ojs.revistas.unitru.edu.pe:article/6190 |
network_acronym_str |
REVUNITRU |
network_name_str |
Revistas - Universidad Nacional de Trujillo |
repository_id_str |
|
spelling |
Evans syndrome and primary biliary cholangitis: A case reportSíndrome de Evans y colangitis biliar primaria: A propósito de un casoCarranza-Castillo, Julio Enrique Paredes-Pizan, Esther Melissa Gutiérrez-Guerrero, Ana Gricelda Murga-Loayza, Piero Alessandro Narcizo-Valderrama, David Paz-Ramos, Betsy Bellisa Neira-Corrales, Yaqui Gretel anemia hemolítica autoinmunepúrpura trombocitopénica idiopáticacirrosis biliar primariacolecistitisautoimmune hemolytic anemiaidiopathic thrombocytopenic purpuraprimary biliary cirrhosischolecystitisIn this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagnosed as dengue with alarm signs due to positive IgG results for this infection; he presented with fever, jaundice with direct predominance of hyperbilirubinemia, anemia, alkaline phosphatase and persistent elevated gamma-glutamyl transpeptidase; for which additional laboratory and imaging tests were performed to consolidate the etiology of the symptoms presented, to finally be diagnosed with both conditions.En este reporte, presentamos el caso de un paciente diagnosticado con síndrome de Evans y colangitis biliar primaria, una combinación inusual que hasta la fecha cuenta con pocos casos reportados en la literatura. El paciente presentó características clínicas complejas, que por datos epidemiológicos se tuvo como primer diagnóstico dengue con signos de alarma por resultados IgG positivo para dicha infección; cursó con fiebre, ictericia con hiperbilirrubinemia a predominio directo, anemia, fosfatasa alcalina y gammaglutamil transpeptidasa elevada persistente; por lo cual adicionalmente se realizaron los exámenes laboratoriales e imagenológicos correspondientes para consolidar la etiología de la sintomatología presentada, para finalmente ser diagnosticado con ambas condiciones.Facultad de Medicina2024-12-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://revistas.unitru.edu.pe/index.php/RMT/article/view/6190Revista Médica de Trujillo; Vol. 19 Núm. 4 (2024): REVISTA MÉDICA DE TRUJILLO; 140-1432522-6150reponame:Revistas - Universidad Nacional de Trujilloinstname:Universidad Nacional de Trujilloinstacron:UNITRUspahttps://revistas.unitru.edu.pe/index.php/RMT/article/view/6190/6296Derechos de autor 2024 "Los autores conservarán sus derechos de autor y garantizarán a la revista el derecho de primera publicación de su obra"https://creativecommons.org/licenses/by-nc/4.0/info:eu-repo/semantics/openAccessoai:ojs.revistas.unitru.edu.pe:article/61902025-01-01T00:06:22Z |
dc.title.none.fl_str_mv |
Evans syndrome and primary biliary cholangitis: A case report Síndrome de Evans y colangitis biliar primaria: A propósito de un caso |
title |
Evans syndrome and primary biliary cholangitis: A case report |
spellingShingle |
Evans syndrome and primary biliary cholangitis: A case report Carranza-Castillo, Julio Enrique anemia hemolítica autoinmune púrpura trombocitopénica idiopática cirrosis biliar primaria colecistitis autoimmune hemolytic anemia idiopathic thrombocytopenic purpura primary biliary cirrhosis cholecystitis |
title_short |
Evans syndrome and primary biliary cholangitis: A case report |
title_full |
Evans syndrome and primary biliary cholangitis: A case report |
title_fullStr |
Evans syndrome and primary biliary cholangitis: A case report |
title_full_unstemmed |
Evans syndrome and primary biliary cholangitis: A case report |
title_sort |
Evans syndrome and primary biliary cholangitis: A case report |
dc.creator.none.fl_str_mv |
Carranza-Castillo, Julio Enrique Paredes-Pizan, Esther Melissa Gutiérrez-Guerrero, Ana Gricelda Murga-Loayza, Piero Alessandro Narcizo-Valderrama, David Paz-Ramos, Betsy Bellisa Neira-Corrales, Yaqui Gretel |
author |
Carranza-Castillo, Julio Enrique |
author_facet |
Carranza-Castillo, Julio Enrique Paredes-Pizan, Esther Melissa Gutiérrez-Guerrero, Ana Gricelda Murga-Loayza, Piero Alessandro Narcizo-Valderrama, David Paz-Ramos, Betsy Bellisa Neira-Corrales, Yaqui Gretel |
author_role |
author |
author2 |
Paredes-Pizan, Esther Melissa Gutiérrez-Guerrero, Ana Gricelda Murga-Loayza, Piero Alessandro Narcizo-Valderrama, David Paz-Ramos, Betsy Bellisa Neira-Corrales, Yaqui Gretel |
author2_role |
author author author author author author |
dc.subject.none.fl_str_mv |
anemia hemolítica autoinmune púrpura trombocitopénica idiopática cirrosis biliar primaria colecistitis autoimmune hemolytic anemia idiopathic thrombocytopenic purpura primary biliary cirrhosis cholecystitis |
topic |
anemia hemolítica autoinmune púrpura trombocitopénica idiopática cirrosis biliar primaria colecistitis autoimmune hemolytic anemia idiopathic thrombocytopenic purpura primary biliary cirrhosis cholecystitis |
description |
In this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagnosed as dengue with alarm signs due to positive IgG results for this infection; he presented with fever, jaundice with direct predominance of hyperbilirubinemia, anemia, alkaline phosphatase and persistent elevated gamma-glutamyl transpeptidase; for which additional laboratory and imaging tests were performed to consolidate the etiology of the symptoms presented, to finally be diagnosed with both conditions. |
publishDate |
2024 |
dc.date.none.fl_str_mv |
2024-12-31 |
dc.type.none.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.none.fl_str_mv |
https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190 |
url |
https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190 |
dc.language.none.fl_str_mv |
spa |
language |
spa |
dc.relation.none.fl_str_mv |
https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190/6296 |
dc.rights.none.fl_str_mv |
https://creativecommons.org/licenses/by-nc/4.0/ info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by-nc/4.0/ |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Facultad de Medicina |
publisher.none.fl_str_mv |
Facultad de Medicina |
dc.source.none.fl_str_mv |
Revista Médica de Trujillo; Vol. 19 Núm. 4 (2024): REVISTA MÉDICA DE TRUJILLO; 140-143 2522-6150 reponame:Revistas - Universidad Nacional de Trujillo instname:Universidad Nacional de Trujillo instacron:UNITRU |
instname_str |
Universidad Nacional de Trujillo |
instacron_str |
UNITRU |
institution |
UNITRU |
reponame_str |
Revistas - Universidad Nacional de Trujillo |
collection |
Revistas - Universidad Nacional de Trujillo |
repository.name.fl_str_mv |
|
repository.mail.fl_str_mv |
|
_version_ |
1845253352448851968 |
score |
13.088272 |
Nota importante:
La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).
La información contenida en este registro es de entera responsabilidad de la institución que gestiona el repositorio institucional donde esta contenido este documento o set de datos. El CONCYTEC no se hace responsable por los contenidos (publicaciones y/o datos) accesibles a través del Repositorio Nacional Digital de Ciencia, Tecnología e Innovación de Acceso Abierto (ALICIA).