Evans syndrome and primary biliary cholangitis: A case report

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In this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagno...

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Detalles Bibliográficos
Autores: Carranza-Castillo, Julio Enrique, Paredes-Pizan, Esther Melissa, Gutiérrez-Guerrero, Ana Gricelda, Murga-Loayza, Piero Alessandro, Narcizo-Valderrama, David, Paz-Ramos, Betsy Bellisa, Neira-Corrales, Yaqui Gretel
Formato: artículo
Fecha de Publicación:2024
Institución:Universidad Nacional de Trujillo
Repositorio:Revistas - Universidad Nacional de Trujillo
Lenguaje:español
OAI Identifier:oai:ojs.revistas.unitru.edu.pe:article/6190
Enlace del recurso:https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190
Nivel de acceso:acceso abierto
Materia:anemia hemolítica autoinmune
púrpura trombocitopénica idiopática
cirrosis biliar primaria
colecistitis
autoimmune hemolytic anemia
idiopathic thrombocytopenic purpura
primary biliary cirrhosis
cholecystitis
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spelling Evans syndrome and primary biliary cholangitis: A case reportSíndrome de Evans y colangitis biliar primaria: A propósito de un casoCarranza-Castillo, Julio Enrique Paredes-Pizan, Esther Melissa Gutiérrez-Guerrero, Ana Gricelda Murga-Loayza, Piero Alessandro Narcizo-Valderrama, David Paz-Ramos, Betsy Bellisa Neira-Corrales, Yaqui Gretel anemia hemolítica autoinmunepúrpura trombocitopénica idiopáticacirrosis biliar primariacolecistitisautoimmune hemolytic anemiaidiopathic thrombocytopenic purpuraprimary biliary cirrhosischolecystitisIn this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagnosed as dengue with alarm signs due to positive IgG results for this infection; he presented with fever, jaundice with direct predominance of hyperbilirubinemia, anemia, alkaline phosphatase and persistent elevated gamma-glutamyl transpeptidase; for which additional laboratory and imaging tests were performed to consolidate the etiology of the symptoms presented, to finally be diagnosed with both conditions.En este reporte, presentamos el caso de un paciente diagnosticado con síndrome de Evans y colangitis biliar primaria, una combinación inusual que hasta la fecha cuenta con pocos casos reportados en la literatura. El paciente presentó características clínicas complejas, que por datos epidemiológicos se tuvo como primer diagnóstico dengue con signos de alarma por resultados IgG positivo para dicha infección; cursó con fiebre, ictericia con hiperbilirrubinemia a predominio directo, anemia, fosfatasa alcalina y gammaglutamil transpeptidasa elevada persistente; por lo cual adicionalmente se realizaron los exámenes laboratoriales e imagenológicos correspondientes para consolidar la etiología de la sintomatología presentada, para finalmente ser diagnosticado con ambas condiciones.Facultad de Medicina2024-12-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://revistas.unitru.edu.pe/index.php/RMT/article/view/6190Revista Médica de Trujillo; Vol. 19 Núm. 4 (2024): REVISTA MÉDICA DE TRUJILLO; 140-1432522-6150reponame:Revistas - Universidad Nacional de Trujilloinstname:Universidad Nacional de Trujilloinstacron:UNITRUspahttps://revistas.unitru.edu.pe/index.php/RMT/article/view/6190/6296Derechos de autor 2024 "Los autores conservarán sus derechos de autor y garantizarán a la revista el derecho de primera publicación de su obra"https://creativecommons.org/licenses/by-nc/4.0/info:eu-repo/semantics/openAccessoai:ojs.revistas.unitru.edu.pe:article/61902025-01-01T00:06:22Z
dc.title.none.fl_str_mv Evans syndrome and primary biliary cholangitis: A case report
Síndrome de Evans y colangitis biliar primaria: A propósito de un caso
title Evans syndrome and primary biliary cholangitis: A case report
spellingShingle Evans syndrome and primary biliary cholangitis: A case report
Carranza-Castillo, Julio Enrique
anemia hemolítica autoinmune
púrpura trombocitopénica idiopática
cirrosis biliar primaria
colecistitis
autoimmune hemolytic anemia
idiopathic thrombocytopenic purpura
primary biliary cirrhosis
cholecystitis
title_short Evans syndrome and primary biliary cholangitis: A case report
title_full Evans syndrome and primary biliary cholangitis: A case report
title_fullStr Evans syndrome and primary biliary cholangitis: A case report
title_full_unstemmed Evans syndrome and primary biliary cholangitis: A case report
title_sort Evans syndrome and primary biliary cholangitis: A case report
dc.creator.none.fl_str_mv Carranza-Castillo, Julio Enrique
Paredes-Pizan, Esther Melissa
Gutiérrez-Guerrero, Ana Gricelda
Murga-Loayza, Piero Alessandro
Narcizo-Valderrama, David
Paz-Ramos, Betsy Bellisa
Neira-Corrales, Yaqui Gretel
author Carranza-Castillo, Julio Enrique
author_facet Carranza-Castillo, Julio Enrique
Paredes-Pizan, Esther Melissa
Gutiérrez-Guerrero, Ana Gricelda
Murga-Loayza, Piero Alessandro
Narcizo-Valderrama, David
Paz-Ramos, Betsy Bellisa
Neira-Corrales, Yaqui Gretel
author_role author
author2 Paredes-Pizan, Esther Melissa
Gutiérrez-Guerrero, Ana Gricelda
Murga-Loayza, Piero Alessandro
Narcizo-Valderrama, David
Paz-Ramos, Betsy Bellisa
Neira-Corrales, Yaqui Gretel
author2_role author
author
author
author
author
author
dc.subject.none.fl_str_mv anemia hemolítica autoinmune
púrpura trombocitopénica idiopática
cirrosis biliar primaria
colecistitis
autoimmune hemolytic anemia
idiopathic thrombocytopenic purpura
primary biliary cirrhosis
cholecystitis
topic anemia hemolítica autoinmune
púrpura trombocitopénica idiopática
cirrosis biliar primaria
colecistitis
autoimmune hemolytic anemia
idiopathic thrombocytopenic purpura
primary biliary cirrhosis
cholecystitis
description In this report, we present the case of a patient diagnosed with Evans syndrome and primary biliary cholangitis, an unusual combination that to date has few cases reported in the literature. The patient presented complex clinical characteristics, which, based on epidemiological data, was first diagnosed as dengue with alarm signs due to positive IgG results for this infection; he presented with fever, jaundice with direct predominance of hyperbilirubinemia, anemia, alkaline phosphatase and persistent elevated gamma-glutamyl transpeptidase; for which additional laboratory and imaging tests were performed to consolidate the etiology of the symptoms presented, to finally be diagnosed with both conditions.
publishDate 2024
dc.date.none.fl_str_mv 2024-12-31
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190
url https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv https://revistas.unitru.edu.pe/index.php/RMT/article/view/6190/6296
dc.rights.none.fl_str_mv https://creativecommons.org/licenses/by-nc/4.0/
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by-nc/4.0/
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Facultad de Medicina
publisher.none.fl_str_mv Facultad de Medicina
dc.source.none.fl_str_mv Revista Médica de Trujillo; Vol. 19 Núm. 4 (2024): REVISTA MÉDICA DE TRUJILLO; 140-143
2522-6150
reponame:Revistas - Universidad Nacional de Trujillo
instname:Universidad Nacional de Trujillo
instacron:UNITRU
instname_str Universidad Nacional de Trujillo
instacron_str UNITRU
institution UNITRU
reponame_str Revistas - Universidad Nacional de Trujillo
collection Revistas - Universidad Nacional de Trujillo
repository.name.fl_str_mv
repository.mail.fl_str_mv
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score 13.088272
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