Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report

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Budd-Chiari syndrome is caused by an obstruction of blood flow to the liver. Published cases of the antiphospholipid syndrome associated with BCS are limited in the pediatric population. We report a 15-year-old adolescent who presented with fever, ascites, and hepatosplenomegaly. Hepatic Doppler ult...

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Autores: Atamari-Anahui, Noé, Domínguez-Rojas, Jesús, Ruiz-Solsol, Luis, López-Turpo, Maryori, Castillo-Delgadillo, Amarilis, Quiñonez Saif, David, Campano, William
Formato: artículo
Fecha de Publicación:2022
Institución:Sociedad de Gastroenterología del Perú
Repositorio:Revista de Gastroenterología del Perú
Lenguaje:español
OAI Identifier:oai:ojs.revistagastroperu.com:article/1333
Enlace del recurso:http://www.revistagastroperu.com/index.php/rgp/article/view/1333
Nivel de acceso:acceso abierto
Materia:Antiphospholipid syndrome
Child
Lupus erythematosus
systemic
Budd-Chiari syndrome
Síndrome Antifosfolípido
Niño
Lupus Eritematoso Sistémico
Síndrome de Budd-Chiari
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spelling Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case reportSíndrome de Budd Chiari secundario al síndrome antifosfolipídico y lupus eritematoso sistémico en una adolescente: reporte de un casoAtamari-Anahui, NoéDomínguez-Rojas, JesúsRuiz-Solsol, LuisLópez-Turpo, MaryoriCastillo-Delgadillo, AmarilisQuiñonez Saif, DavidCampano, WilliamAntiphospholipid syndromeChildLupus erythematosussystemicBudd-Chiari syndromeSíndrome AntifosfolípidoNiñoLupus Eritematoso SistémicoSíndrome de Budd-ChiariBudd-Chiari syndrome is caused by an obstruction of blood flow to the liver. Published cases of the antiphospholipid syndrome associated with BCS are limited in the pediatric population. We report a 15-year-old adolescent who presented with fever, ascites, and hepatosplenomegaly. Hepatic Doppler ultrasound revealed no flow in the right and middle hepatic veins and in the inferior vena cava. Abdominal tomography revealed extensive thrombosis of the inferior vena cava. During hospitalization, she was diagnosed with antiphospholipid syndrome and systemic lupus erythematosus. She was given treatment with unfractionated heparin, low molecular weight heparin, and anticoagulants. Budd-Chiari syndrome secondary to the antiphospholipid syndrome is a life-threatening disease. Timely diagnosis and treatment improve the quality of life of the patient.El síndrome de Budd-Chiari es causado por una obstrucción del flujo sanguíneo del hígado. Los casos publicados del síndrome antifosfolípido asociado a SBC son limitados en la población pediátrica. Reportamos el caso de una adolescente de 15 años que presentó fiebre, ascitis y hepatoesplenomegalia. En la ecografía Doppler hepática se observó ausencia de flujo en la vena hepática derecha y media, y en la vena cava inferior. En la tomografía abdominal se observó una extensa trombosis de la vena cava inferior. Durante la hospitalización se le diagnosticó SAF y lupus eritematoso sistémico. Se le administró tratamiento con heparina no fraccionada, heparina de bajo peso molecular y anticoagulantes. El síndrome de Budd-Chiari secundario al síndrome antifosfolípido es una enfermedad potencialmente mortal. El diagnóstico y el tratamiento oportunos permiten mejorar la calidad de vida del paciente.Sociedad de Gastroenterología del Perú2022-06-30info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttp://www.revistagastroperu.com/index.php/rgp/article/view/133310.47892/rgp.2022.422.1333Revista de Gastroenterología del Perú; Vol. 42 Núm. 2 (2022); 131-1351609-722X1022-5129reponame:Revista de Gastroenterología del Perúinstname:Sociedad de Gastroenterología del Perúinstacron:SOCIOGASTROspahttp://www.revistagastroperu.com/index.php/rgp/article/view/1333/1130Derechos de autor 2022 Revista de Gastroenterología del Perúinfo:eu-repo/semantics/openAccessoai:ojs.revistagastroperu.com:article/13332023-01-14T23:58:54Z
dc.title.none.fl_str_mv Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
Síndrome de Budd Chiari secundario al síndrome antifosfolipídico y lupus eritematoso sistémico en una adolescente: reporte de un caso
title Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
spellingShingle Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
Atamari-Anahui, Noé
Antiphospholipid syndrome
Child
Lupus erythematosus
systemic
Budd-Chiari syndrome
Síndrome Antifosfolípido
Niño
Lupus Eritematoso Sistémico
Síndrome de Budd-Chiari
title_short Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
title_full Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
title_fullStr Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
title_full_unstemmed Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
title_sort Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
dc.creator.none.fl_str_mv Atamari-Anahui, Noé
Domínguez-Rojas, Jesús
Ruiz-Solsol, Luis
López-Turpo, Maryori
Castillo-Delgadillo, Amarilis
Quiñonez Saif, David
Campano, William
author Atamari-Anahui, Noé
author_facet Atamari-Anahui, Noé
Domínguez-Rojas, Jesús
Ruiz-Solsol, Luis
López-Turpo, Maryori
Castillo-Delgadillo, Amarilis
Quiñonez Saif, David
Campano, William
author_role author
author2 Domínguez-Rojas, Jesús
Ruiz-Solsol, Luis
López-Turpo, Maryori
Castillo-Delgadillo, Amarilis
Quiñonez Saif, David
Campano, William
author2_role author
author
author
author
author
author
dc.subject.none.fl_str_mv Antiphospholipid syndrome
Child
Lupus erythematosus
systemic
Budd-Chiari syndrome
Síndrome Antifosfolípido
Niño
Lupus Eritematoso Sistémico
Síndrome de Budd-Chiari
topic Antiphospholipid syndrome
Child
Lupus erythematosus
systemic
Budd-Chiari syndrome
Síndrome Antifosfolípido
Niño
Lupus Eritematoso Sistémico
Síndrome de Budd-Chiari
description Budd-Chiari syndrome is caused by an obstruction of blood flow to the liver. Published cases of the antiphospholipid syndrome associated with BCS are limited in the pediatric population. We report a 15-year-old adolescent who presented with fever, ascites, and hepatosplenomegaly. Hepatic Doppler ultrasound revealed no flow in the right and middle hepatic veins and in the inferior vena cava. Abdominal tomography revealed extensive thrombosis of the inferior vena cava. During hospitalization, she was diagnosed with antiphospholipid syndrome and systemic lupus erythematosus. She was given treatment with unfractionated heparin, low molecular weight heparin, and anticoagulants. Budd-Chiari syndrome secondary to the antiphospholipid syndrome is a life-threatening disease. Timely diagnosis and treatment improve the quality of life of the patient.
publishDate 2022
dc.date.none.fl_str_mv 2022-06-30
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv http://www.revistagastroperu.com/index.php/rgp/article/view/1333
10.47892/rgp.2022.422.1333
url http://www.revistagastroperu.com/index.php/rgp/article/view/1333
identifier_str_mv 10.47892/rgp.2022.422.1333
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv http://www.revistagastroperu.com/index.php/rgp/article/view/1333/1130
dc.rights.none.fl_str_mv Derechos de autor 2022 Revista de Gastroenterología del Perú
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Derechos de autor 2022 Revista de Gastroenterología del Perú
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedad de Gastroenterología del Perú
publisher.none.fl_str_mv Sociedad de Gastroenterología del Perú
dc.source.none.fl_str_mv Revista de Gastroenterología del Perú; Vol. 42 Núm. 2 (2022); 131-135
1609-722X
1022-5129
reponame:Revista de Gastroenterología del Perú
instname:Sociedad de Gastroenterología del Perú
instacron:SOCIOGASTRO
instname_str Sociedad de Gastroenterología del Perú
instacron_str SOCIOGASTRO
institution SOCIOGASTRO
reponame_str Revista de Gastroenterología del Perú
collection Revista de Gastroenterología del Perú
repository.name.fl_str_mv
repository.mail.fl_str_mv
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score 13.0672035
Budd Chiari syndrome secondary to antiphospholipid syndrome and systemic lupus erythematosus in an adolescent: a case report
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