Primitive peripheral neuroectodermal tumor of the kidney, case report.

• Autores: Bustamante Chávez , Rubí X., Yalta Arce , Herman, Vásquez Sullca , Roy Roger
• Formato: artículo
• Fecha de Publicación: 2023
• Institución: Cuerpo Médico Hospital Nacional Almanzor Aguinaga Asenjo
• Repositorio: Revista del Cuerpo Médico Hospital Nacional Almanzor Aguinaga Asenjo
• Lenguaje: español
• OAI Identifier: oai:cmhnaaa_ojs_cmhnaaa.cmhnaaa.org.pe:article/1377
• Enlace del recurso: https://cmhnaaa.org.pe/ojs/index.php/rcmhnaaa/article/view/1377
• Nivel de acceso: acceso abierto
• Materia: Tumor neuroectodérmico periférico primitivo; Riñón; Enfermedad rara; Nefrectomía; Informes de Casos; Perú; Kidney; Rare disease; Nephrectomy; Case Reports; Peru; Neuroectodermal Tumors, Primitive, Peripheral

Introduction: Peripheral primitive neuroectodermal tumor of the kidney (PNETk) is a very aggressive rare disease that mainly affects young men. Case report: A 19-year-old male patient with symptoms of abdominal pain, hematuria and a palpable mass, the tomography shows a large left renal tumor. Conventional radical nephrectomy was performed and sent for pathology study plus histochemistry, resulting in PNETk. The patient then continued his oncology management for chemotherapy initially. Conclusion: The PNETk that we describe represents the first case reported in our country, it constitutes a unique clinical entity due to its rarity, being a challenge to make a diagnosis and its behavior and management is still based on case reports due to its infrequency.